UtanoZvirwere uye Conditions

The etiology kuti sarcoidosis uye chii nezvirwere zviri kuvhiringidzwa urwere Lefgrena

Lefgrena chirwere - zvakafanana, ichibata hilar nodes bronchopulmonary nhengo dzinobudisa maitiro kumativi ose. Chirwere achiperekedzwa ganda kuratidzwa (erythema nodosum), fivha, uye arthralgia. Zviratidzo izvi ndiwo runozivisa sarcoidosis.

Kana chirwere chinobata yakasiyana nhengo - nomumapapu, chirwatata, node nodes. Lefgrena chirwere sarcoidosis asina zvitange uye haisi chinotapuriranwa chirwere. Chisingafaniri kuvhiringidzwa oncologic chirwere pezvakaitwa uye TB.

zvekuchipatara mufananidzo

Sarcoidosis kwave chaizvo kwenguva refu isingawanzowanikwi chirwere, asi nhasi zvinhu yachinja, zvokurwara rinopararira panguva nokukurumidza mwero munyika. Maererano nenhamba, kupfuura ani zvake kutamburira chirwere Lefgrena vakadzi 20 kusvika 40 makore, asi chirwere unogona kuuya munhu.

Zvinogona kuitika pasina zviratidzo, zvishoma nezvishoma kana iri rikwanise muchimiro. Kazhinji Asymptomatic kiriniki dzakaonekwa netsaona musi chokudzivirira fluorography ongororo. Rakajairika iri zvishoma nezvishoma kunoita chirwere uye zvinotevera zviratidzo:

  • dyspnea pamusoro nesimba;
  • munhu patainzwa kurwadza ari mubhokisi;
  • marwadzo pakati pamafudzi mashizha ;
  • chikosoro yakaoma;
  • nefivha yakaderera-vegiredhi ;
  • kuneta uye utera;
  • kunyanya vangadikitira;
  • kurasikirwa havi;
  • kurwadza kwemajoini panzvimbo dzapasi musana.

Chenjera kuti sarcoidosis inonzi urwere Lefgrena, zvinonzi pamwe nokumutsa tembiricha kuti 38-39 ° C, kurwadza kwemajoini, ganda maronda muchimiro erythema, chipfuva marwadzo uye kupfupika mweya. Hazvishamisi mu chenjera panguva kupora zvizere pasina kushandiswa kwevanhu marapirwo nezvimwe kupindira.

The etiology chirwere

Kusvikira pakuguma mushonga anozivikanwa zvinokonzera chirwere ichi, zvingangoita kuti vanotsamwisa nokuda zvinhu zvinotevera zvingamuka:

  • chirwere, Mycobacterium tibhii, hepatitis C;
  • yaivhuvhuta zvimwewo zvinoitika, Kufema simbi guruva;
  • kusvuta, iyo haisi honzeri, asi zvikuru zvinoomesa weboka chirwere;
  • nhodzera.

Kudzivirira sarcoidosis

Sick chirwere Lefgrena chakakosha kurega kusvuta, kuti rikurumidze apore. Zvakakodzera nguva yokuongorora nhengo pechipfuva muna 2 years. Kufungisisa ndechokuti etiology chirwere Hazvizivikanwi kusvikira pakuguma, nenhungamiro chokudzivirira chiito kuti kukudziridzwa. Nyanzvi vanokurudzira kuti usagunzva simbi guruva uye foci chirwere.

Lefgrena chirwere sarcoidosis dzakaonekwa kutevera extrapulmonary localization rikurumidze - kukunda subcutaneous zvinyama, ganda uye peripheral node nodes. Pane kuwedzera remuromo, subclavian, axillary uye inguinal nodes. Mune zvimwe zviitiko, dzakachinja node nodes ari mudumbu.

Bone uye nechepakati tsinga vari kukanganiswa ndoda kakawanda, asi zvakaoma kuti chirwere kuitika. Sarcoidosis mwoyo kunoitika muna 20-30% nyaya dziri asymptomatic. Left divi mwoyo vari wakaderedzwa bhuku, zvakarurama ventricle inowedzerawo.

Early kuongororwa uye kurapwa rakapiwa mukana kuvimba yakanaka mugumisiro. Mune imwe nyaya, pane kuchinja zvemapapu rinenge iyo pakupedzisira inotungamirira kuremara.

Lefgrena chirwere chenjera sarcoidosis musimboti

Kazhinji kuvhiringidzwa sarcoidosis, tiibhii nokuda kufanana zviratidzo. Izvi zvinoda kwazvo kuongororwa, nekuti zvinokonzera uye siyana kurapa. Hapana nyaya haagoni kuita kuzvidzora kurapwa, kunyanya kutora zvinodhaka vaida kuti varwere neTB, zvinogona kutungamirira kurufu.

Lefgrena syndrome (munhu chaiwo muenzaniso) - iri apo murwere rwevanhu ezvinhu ndiyo inogutsa kupima. Pane kuchinja paganda. Kuonekwe:

  • papules uye plaques;
  • Chilblains lupus;
  • keloid mavanga;
  • infiltrates;
  • erythema nodosum;
  • SKD uye CKD sarcoid Beck;
  • mazhinji gobvu nodes ari subcutaneous tishu.

Diagnostics

Maonero wevarwere Lefgrena chirwere ndiko kuita X-ray. Sezvo chakagadziridzwa nzira uchishandisa computed tomography. Muperekedzei nemakemikari uye ropa count.

Dambudziko kurapwa ndiko kudzvinyirira kushoma. Chinonyanya vakarongeka nzira kushandiswa corticosteroids kwemwedzi mitanhatu. Kana zvinokanganisawo zvinokosha zvomukati chinodikanwa glucocorticosteroid kemikari mishonga.

Nokukurumidza mberi kosi ikarapwa pamwe vachiravana pfupi pamusoro intravenous kwokubatsira Anti-anogumbura zvinodhaka. Muzviitiko apo mishonga iri simba, vakabata plasmapheresis (ropa yokuzvinatsa). Panguva chakakomba Danho zvirwere zvemapapu zvinoda nhego kuisirwa. Course chirwere uye kurapwa zvaizoitika zvikurukuru zvakanaka, asi haumanikidzwi kutanga muitiro.

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