Retinitis pigmentosa: zviratidzo, kurapwa

To musi, pane hosha dzakawanda ziso. Vamwe vavo vari vawana zvakasikwa, apo vamwe vari nhaka uye vari panoonekwa anenge kubva pakuberekwa.

Nyaya ino kutaura pamusoro chirwere, raiva wechipiri boka uye anonzi "retinitis pigmentosa". Tichanzwisisa chii chinokonzera kutsamwisa chavapo, uye kurukura kana pane nzira inobudirira kubvisa dambudziko.

Chii retinitis pigmentosa

Hosha iri nhaka retinal zvokurwara, panguva iyo munhu photoreceptor uye ruvara epithelium rukoko chinhu pave chinopedza kuchinja uye Homwe vari kuumbwa maererano mhando mapfupa masero.

Kazhinji, retinitis pigmentosa anoita pacharo vainzwa vaduku kana mwana asina makore 8, uye anotanga nokushingaira mberi. It vanotyisidzira murwere bofu makore 40-60.

Zvinokonzera chirwere

Kukonzera retinitis pigmentosa chinhu vakawanda Gene kunotouraya zviri kukonzera kuti kwetunhu uye nokugoverana wakananga mapuroteni panguva fetus.

Panguva iyoyo akataura chikuru nzira pakukura chirwere:

1. Related pasi. Panyaya iyi, iyo zvokurwara wabva mai mwanakomana, pamwe X chromosome.
2. Autosomal recessive. Zvokurwara iri kubva vabereki vaviri kuti mwana panguva iyoyo.
3. Autosomal zvakazara. Zvokurwara iri chinopfuudzwa kubva mumwe vabereki mwana.

Pane mamiriro ezvinhu kana retinitis pigmentosa kunokwanisa kuonekwa Varwere izvi, imwe mhuri ane chirwere haina kuitika adarika. Asi zviitiko zvakadaro hadziwanzowaniki. Kazhinji, asi zvokurwara nhaka uye kunokanganisa nezvizvarwa zvevazukuru imwe mhuri.

Zvikurukuru pangozi vana vakaberekwa muwanano blizkokrovnom panguva iyo anowedzera zvikuru ndingangokuvara dzakasiyana-siyana Gene kunotouraya.

Kupatsanura pakati retinitis pigmentosa

Zvichienderana chirwere uye vawirwa nenjodzi, musiyano kaviri chirwere:

1. Typical. In chimiro ichi kutarisana acuity (zvose peripheral uye nechepakati) inochengeterwa kwenguva refu ari chakaipa siyana. Kunyange zvazvo panguva ino hapana kare kukundwa tsvimbo-maitiro uye kwaita foci kuti ruvara kuunganidza mune dzimwe nzvimbo yacho fundus.

2. Atypical. chimiro ichi ane mhando dzakawanda:

• Amelanotic retinitis. Panguva iyi mhando fundus hapana ruvara masero. Zvisinei, pane vamwe zviratidzo chirwere.
• Sectoral chidhongi retinitis pigmentosa. Photos kuratidza kuvapo retinal pigmented foci kusimbiswa munhu dhipatimendi fundus uye pachiimbwa ine chidhongi chimiro. In chirwere ichi, zviratidzo zvingava aisatombowanika kana wakazvichengeta anononoka chaizvo chokubuda.
• Belotochechny. Panguva chimiro ichi fundus vakachengeta mavara akawanda chena. Zviratidzo izvi zvakafanana panguva retinitis pigmentosa.
• Inverted. In chimiro ichi chirwere inotanga retinal maronda ari nechepakati chikamu, kukanganisa gadziriro cone. The muitiro achabatsirwa kukura photophobia uye nokukurumidza Kuipa nechepakati chiratidzo.

Zviratidzo zviri chirwere

Apo chirwere akadai retinitis pigmentosa, Photo ziso akagamuchira panguva ophthalmoscopy, ratidza kuvapo vatatu mamirire zvinhu:

1. Atrophy of retinal ruvara epithelium. Muchiitiko chino, pane ari kuderedza worudzi ruduku arteries uye pakuonekwa chena ruvara mavara.
2. Optic Disc anova zvinooneka paler.
3. On arikunze pamusoro fundus uye weboka mutsinga diki ngapaonekwe vanonzi "pfupa corpuscles."

zviratidzo

Kuchinja api achiperekedzwa retinitis pigmentosa? Zviratidzo zvingasanganisira zvinotevera:

• usiku upofu ( "upofu") anokonzerwa chinopedza mananara ari the retina;
• kusashivirirana kudzvokora;
• madzerere;
• rutapudzo pamusoro peripheral chiratidzo ;
• nematambudziko pameso enyu kuchinjira murima muimba pashure kwakarivhenekera, ndiEzekieri;
• usiku-upofu.

Atypical siyana vanogona anowedzera kuti pamwe photophobia uye ungaderedza ruvara zvawakaratidzwa.

chirwere chirwere

Chirwere kuti retinitis pigmentosa anobata ophthalmologist. Izvi zvinoitika nokuda anamnesis, pazviri pachena kana mamiriro akadaro runenge rimwe chinotevera hama. Mukuwedzera, ongororo kurasikirwa photoreceptor sero emuchina vachishandisa electroretinography uye kutarisana yokuedzwa.

Kuvapo chinoratidza retinitis pigmented foci anogona kuonekwa nokuda mufambiro ophthalmoscopy uye fundus mapikicha aita.

Kuzivisa kuvapo urema muziso fundus, uye pamberi ruvara epithelium atrophy uye macular edema munzvimbo uchishandisa fluorescence yacho the retina angiography (FAG).

Uyewo, rinorondedzerwa ruvara chiratidzo, rima kwadzakabva uye musiyano aikanganiswa pamwero.

Mabatirwo retinitis pigmentosa

Zvinoita kubvisa zvirwere zvakadai retinitis pigmentosa? Treatment zvakagadzirirwa nhasi, zvinosuruvarisa usingabviri zvachose kubvisa dambudziko. Chinhu bedzi anogona kubatsira vanachiremba - ndiko kubvisa zvimwe zviratidzo chirwere.

In pamberi macular edema riri basa negashiro diuretics, izvo zvinosanganisira carbonic anhydrase FIs.

cataract rinobviswa Via kuvhiyiwa.

Photocoagulation nokuti vanachiremba vascular vanokurudzira kugamuchirwa vascular pharmacological nevamiririri.

Uyezve, vhitamini amakavaitira kusimbisa negashiro nicotinic acid. Uyewo, pane maonero kuti nedanho kudzikira zvinogona seiyi pasi kuwedzera kudya vhitamini A, iyo inogona kuwanikwa zvakasiyana Mishonga zvokuwedzera.

Uyezve, varwere vari zano kupfeka Sunglasses inokosha kuti zvichaita Sechipanji rezuva orangy nemwaranzi. Izvi zvichabatsira kuchengetedza the retina kubva kukuvara.

Zvataurwa mushonga chichabatsira kurerutsa mwero kunoita zvirwere zvakadai retinitis pigmentosa. Treatment acho mishonga iyi inogona kushandiswa chete muchimiro zvikuru dzakabudirira zvokudya abvume, iyo inopa shoma shoma purine yeimwe uye remafuta akawandisa zvokudya. Uyezve, zviri chinodiwa kuti zvinyorwe zvaunodya blueberries, sezvo iri dzinongoitika antioxidant uye zvitubu vhitamini A.

Imwe nzira ndichiva kubvisa matambudziko akadai, akadai retinitis pigmentosa - chokumisa muchitokisi mishonga. Nzira iyi pari pasi rinoita kukura, asi masayendisiti akavimbisa kuti munguva yemberi zvichaita vatanga vanoshingaira kudzidzira uye rinoshandiswa pachiimbwa dzimwe zvinoumba mishonga.

Pfungwa iyi mhando kurapwa achava seizvi. Kubva hunde masero ane Gene utano hunokosha mumarabhoritari kuchawedzera masero retinal. Next vachapiwa muchibereko varwere retinitis pigmentosa kudzokera pamberi pavo. Panyaya iyi, kuti dziviriro yezvirwere mumuviri chero zvazvingava kuramba kudyara, sezvazvakanyorwa kubva murwere pachake hunde masero.

Kunyange zvazvo pakutanga matanho kurutivi kuzadzika ndaviga chinangwa kunge vatora kusvika pokuti nzira iyi unotanga inoshandiswa pakurapa zvirwere ziso, achiri kure, nhasi kare.

Nzira kukura muzvidzivirire zvirwere

Sezvo retinitis pigmentosa, kakawanda ndepana majini vanochiva kudzivisa kuonekwa, zvinosuruvarisa haabudiriri. Chinhu bedzi anogona kuita murwere mumamiriro ezvinhu akadaro - napo kunetesa muitiro okukura matambudziko uye kunonotsa nguva kutanga upofu.

Kuti aite izvi, zvakakosha kunyoresa ane ophthalmologist kugara kuzomushanyira uye kuteerera audzwa zvose. Havafaniri kuramba kupfeka inokosha inodzivirira magirazi, izvo achaponesa the retina weziso pashamwari kuona chiedza.

Nokuti vanoda kuverenga, unofanira kusarudza chinonyanya rakakodzera Fonts kuti haatarisiri ziso epfungwa.

Stay utano!