Goodpasture kuti chirwere: Inokonzera, Zviratidzo neMarapirwo Nzira

Goodpasture kuti chirwere - isingawanzowanikwi autoimmune chirwere kuti pamwe Chizvarwa atypical antibodies kuti kurwisa masero mumapapu neitsvo. chirwere Similar runonyanya inokanganisa vanhu pakati pemakore 12 uye 35 okuberekwa. Zvinofungidzirwa kuti vamwe varwere vane majini propensity kune nyonganyonga yakadaro.

Goodpasture kuti chirwere: zvinokonzera chirwere

Chokwadi, murwere munhu ane majini kubatwa kuti chirwere. Kunyange zvakadaro, pane zvinhu chirwise ane autoimmune kuita.

With kukura chirwere dziviriro yezvirwere mumuviri unobereka antibodies kuti urwise basal Kamudzira pamusoro capillaries ose pulmonary Formação de uye renal tubules. Somugumisiro izvi zviri sei uye vakadambura capillaries, zvichikonzera womukati ropa uye chokuita zviratidzo.

Kokutanga chirwere chakadai yakanyorwa 1919. Asi nhasi haisi kuzivikanwa chii kunokonzera masoja mhinduro. Zvinofungidzirwa kuti Goodpasture kuti chirwere kwakabatana zvirwere. Dzimwe nguva activation chirwere kunokonzerwa zvimwe makemikari Inobaya. It rakanyorwawo zviitiko dzinoverengeka umo urwere akatanga kuva pashure pokutora mishonga.

Goodpasture kuti urwere: Zviratidzo

Kazhinji, zviratidzo zvechirwere kufema hurongwa wokutanga. Murwere anonyunyuta muchipfuva marwadzo, kakawanda chikosoro uye kupfupika mweya pamusoro nesimba. Maererano hemoptysis rinotanga kukura chirwere. Mumapapu vanogona kunzwa nyoro kana yakaoma wheezing. Murwere vanogona kugara kuneta uye hope. Dzimwe nguva pane zvinoshamisa uremu nokuda kuderera kwetsandanyama. Kusiyana nezvinofungwa nevakawanda, zviri capillaries mumaziso zvisina kukanganiswa ne chirwere.

Sezvo pane hombe diki ropa, rinotevera chiratidzo - ndiko kupererwa, kana kupererwa neropa. Kana Paunoongorora murwere, zvinogona kuonekwa kuti ganda rake zvakare zvacheneruka. Pane cyanosis pamusoro mucous membranes. Mune zvimwe zviitiko, kuzvimba kumeso kuonekwe. The tembiricha iri kazhinji ichiwedzerwa.

Zviratidzo zvirwere itsvo kuonekwa zvishoma paya. Ungacherechedza kusarudzwa shoma ropa iri weti. Renal kukundikana mberi nokukurumidza uye achabatsirwa warwo zviratidzo.

Goodpasture kuti chirwere: chirwere nzira

Kuti chirwere, chiremba anofanira ukanyatsoongorora murwere kuona migumisiro ECG nemiedzo. Kazhinji, kuongorora ropa kunogona kuonekwa simbi kushaikwa kupererwa neropa uye kwakawedzera leukocyte count, zvakawedzera ESR. Urinalysis anoona weti zvizhinji mapuroteni uye masero matsvuku eropa. Unofanira zvachose kuongorora sputum, sezvazvakanyorwa rinowanikwawo masero matsvuku eropa. Vachava kubatsira uye spirography inobatsira kuona kutyorwa nechitarisiko afemeruke. Ipa zvakare ECG kudzidza magasi ropa, x-mwaranzi uye biopsy pakati zvakakuvadza zvinyama, izvo zvinoita kuti tikwanise kuisa zvachose kuongorora chirwere.

Goodpasture kuti urwere: Kurapwa

Kutaura zvazviri, fungidziro varwere yakadaro zvisingafadzi.. Uye chinonyanya kukosha pano - nguva rokuongorora chirwere uye kutanga kurapwa nokukurumidza.

Zvinosuruvarisa mishonga chaiyo zvirwere zvakadai usipo. Asi akataura kuti kazhinji, zvakakwana kurapa chirwere basa aserera mukati 6-9 mwedzi. Kana unogona kumisa pave renal uye pulmonary chirwere, murwere anogona kurarama. Kazhinji, vanachiremba akarayira zvinoverengeka pakugamuchira corticosteroids. Plasmapheresis rinoitwa, kana zvichikodzera - kuwedzerwa ropa , uye kunyange itsvo transplantation. Kuti kumisa kukura kupererwa neropa uye simbi kushaikwa zvemano varayire mishonga yakakodzera. Asi dzimwe nguva, muna wakakura zvikuru zviitiko, kuwedzerwa ropa inodiwa kuchaitwa kupererwa neropa.