UtanoZvirwere uye Conditions

Mastocytosis kuvana: zvinokonzera, kurapwa uye migumisiro

Vana varware, uye ichi hapana kusiya. Zvakanaka, kana chirwere inomhanya, asiwo zvinoitika kuti ndiye mwana kwemakore akawanda, kana kuipa - hwose. Vakaropafadzwa avo vabereki vanoziva chete sei inoyerera chando uye runny mhino. Munyaya ino tichashandisa kutaura nezvematambudziko aya, tichataura pamusoro chirwere ichi sezvo mastocytosis vana.

Muchidimbu pamusoro chirwere

The chirwere, pakutanga tingaona haakonzeri hanya. Asi zvinokosha kuti sungisa pamwe kurapwa, mwana mumuviri kutanga kuunganidza masero mafuta. Nokufamba kwenguva, mhembwewo chirwere chinogona kuchinja kuva akaipa chimiro.

Mastocytosis hariwanikwi, kazhinji vana vanotambura nawo. Zvinokanganisawo kwete chete ganda, asi dzimwe nhengo. Anenge makumi mapfumbamwe kubva muzana vana chirwere ichi vanotambura urticaria pigmentosa. Panguva kutanga kwekupwanyiwa kana chirwere mastocytosis nevana, mabatiro ndiko kushandiswa antihistamines. Panguva iyi, hazvo kuongororwa nokufamba runotikurudzira chirwere.

Makumi manomwe nezvishanu kubva muzana pacho, hosha rinowanikwa mune vana pasi makore matatu uye hakubvi zvepabonde mwana. The etiology uye pathogenesis haisati ainyatsonzwisisa, uye zvakarurama kunzi mhaka chirwere hazvibviri. Pane pfungwa kuti dzimwe nguva hosha chinopfuudzwa ari autosomal kureva nenzira.

Mhando zvirwere

Inobva zvechadenga chirwere, mastocytosis vana uye vakuru ane zvinotevera chimiro.

  • Skin, mucheche. Kuchengetwa vana makore matatu. The kukundwa zvomukati asipo. Skin rashes Zvibvisike zvachose pakuyaruka uye haangazvidembi kuonekwa. At zvakasimba vakaratidza zviratidzo vanofanira kugadzirisa, uye Chikurukuru, nenguva kurapwa.
  • Cutaneous mastocytosis kuyaruka uye vakuru. Pane visceral, asi haisi kufambira mberi pane imwe chimiro.
  • System. Kakawanda, izvi Chirwere akacherechedza nedzevakuru. Pane kuchinja ganda, mberi womukati kukuvara nenyere.
  • Akaipa chimiro (rechikepe sero neleukemia). Ichi chimiro chirwere ndiyo inenge nguva zvinouraya. Masero Mast vanochinjwa. Ivo zvazvinoita zvomukati uye munyama, kunyanya pfupa uye peripheral ropa. Zvinofanira kurangarirwa kuti ganda kuratidzwa kazhinji chose vasipo.

Mhando ganda maronda

Kune mhando mashanu ganda maronda chirwere.

  • Maculopapular mastocytosis muvana. Photo zvinoratidzwa sei mwana nezviso panguva iyi. mwana ganda iri yakafukidzirwa mavara diki uye papules tsvuku-mashava.
  • Multiple knotted mhando. On ganda vakaumba chaizvo batana nokusunungura mapfundo. Vanogona kuva tsvuku, pink, tsvuku. dhayamita wavo anenge mumwe sendimita, chimiro - hemispherical.
  • Mastocytoma (oga raiva pedyo nebundu). Rinooneka raiva pedyo nebundu. dhayamita ayo maviri nemashanu masendimita. Zvinogona kumeso kana rakawunyana chimiro. Oga mastocytosis muvana kazhinji rikaitika mutumbi, maoko uye mutsipa. Chinonyanya kubatwa ichi Chirwere vacheche.
  • Diffuse. Anotanga kunokanganisa vana vaduku. The ganda maronda vari vakaumba yero mashava ruvara. Kakawanda, zviri riri muhapwa, pakati magaro. Vaonekwe makatsemuka.
  • Teleangiektatichesky mhando. In vana kashoma.

Zvinokonzera chirwere

Sezvo ini ataurwa pamusoro apa, mhinduro kuti aigona kumutsa chirwere chakadaro ngozi kuti zvakaoma chaizvo, sezvo ayo etiology harizivikanwi. Asi harisati zvichibvira kuziva chikuru zvinokonzera mastocytosis muvana. Komorowski akavakamura muzvikwata inobva zera mwana.

  • Vachangoberekwa. The mhaka chirwere anganzi zvokudya allergen. Chiremba chinofanira kuchengetwa ari chiitiko kuti mhuri ndambodzidza aitambura nechirwere ichi.
  • Nendumure (kuti matatu). Chinowedzera kutanga kuonana kwezvakatipoteredza.
  • Vanoenda kukireshi. Kusvikira kumusoro zvose kwezvikonzero, akawedzera kuti zvokutambisa chisimbwa.
  • vana School vanorwara pamusana kunetseka mupfungwa mamiriro, mupfungwa.
  • Teenagers vanowanzotambura pashure iratidzike seiri kubuda. Mumwe zvikonzero zvinosanganisira vatambi.

To mukuru zvinoita kuti anokonzera chirwere, inofanira kusanganisira simba rokuzvidzivirira. Uye vachiri zvinonakidza kuziva kana mumhuri imwe vanotambura kumarudzi akawanda, zvinganzi kudonongodzwa kuti chirwere ane nhaka hunhu.

chirwere zviratidzo

Mastocytosis nevana, kufanana vukosha ine zviratidzo zvayo. Ngatimbotaura pamusoro pavo, kunyange zvazvo kwokutanga chikamu "Types ganda maronda," isu kare kuitwa pamusoro zviratidzo chirwere. Asi sezvo vanoti hazvina kurwadza kuyeuka.

Kuwedzera pakuva mwana anorwara ari misikanzwa, haana kuda kutamba dzose nguva akagadzirira kuva vabereki mumaoko ake zvakawanda:

  • pane zvikuru kuvaviwa;
  • muviri akafukidzwa yakatsvukuruka-rwepingi makwapa;
  • akatsvuka vari dzikwanise matema ane yakajeka kana ropa mvura;
  • kuti mapundu anopararira kusvika hunde, chiso, maoko (pasina nokukurumidza kurapwa);
  • ganda mwana thicken uye tora mumwe yellowish tint.

Miganhu kunge yakabuda idzodzo dziri kuratidzwa pachena, pose asingadi peel they and and kure. Mazuva mashoma pashure chitarisiko tsvuku makwapa kugume shava.

Dzimwe nguva mburwa zvinogona kumisa kukura, asi pane dzimwe nguva apo vose ganda zvinovhiringidzika uye anotanga kupinda yavo zvomukati.

roga chimiro

Roga mastocytoma - ndiyo imwe nebundu aumba kubva pedanda rechikepe mumasero. Iyi mhando rakanyatsojeka zvisingawanzoitiki, asi tinofanira kuziva nezvazvo. Ko oga mastocytosis nevana (kuonekwa mufananidzo) bundu inotungamirwa. It iri mumuviri, kazhinji zviri shure, chipfuva, mutsipa uye emberi. Kutya pachine hakusi zvakakodzera. Statistical Data dzinoratidza kuti muna 90% nyaya gwapa ichi mumwoyo pamwe nguva. By pakuyaruka mwana kunogona zvizere rakadzikadzika. Nokuti ichi Chirwere kwete Tichishivirira kukuru kuvaviwa uye kutyora zvomukati.

Dzimwe nguva yoga chimiro mastocytosis anogona kutora pigmented nevi. Kutungamirira mwana kuti chiremba kuti kubviswa dzidzo. harizovi zvikomborero daze uye havana kugadzirisa dambudziko.

Kana nembudzana rascheshet vanga kana kukuvadza, panzvimbo yayo pane matema.

Diagnostics

I Ndianiko kutaura kuona mastocytosis kuvana, ayo chinokonzera? nyaya idzi dziri mubereko vabereki vakawanda. Chero zvazvingava, havafungi kushanyira nyanzvi hakusi zvakakodzera. Hunodiwa kana kuonekwa yenzvimbo paganda kero wemwana kwachiremba-dermatologist. Achaita rokuongorora uye, kana zvakakodzera, kutumira vamwe vaaishanda navo. Hapana nyaya musatanga pachavo kurapwa kwavo. Pashure pezvose, iwe hauzivi chaizvo zvipi zvakabetsera pakuonekwa mapundu.

Chiremba tichaongorora mwana wako kunyatsotevera. Zvinangwa izvi, izvozvo inowanzoshandiswa Dermatoscope. With midziyo iyi anobvisa zvikanganiso zviri kuongorora chirwere. Pashure paizvozvo, mibvunzo pamusoro mwana achapiwa vabereki. Mhinduro inofanira kuva zvakanaka, zvinokurudzirwa kuyeuka zvose zvichemo vabva mumuromo mevana. Uyezve, sokuongorora kwomurabhoritari chichaitwa. Tinotofanira bvunzo ropa kupfuura Ultrasound Diagnostics kuti nhengo dzomukati kuitira kudzivisa systemic chimiro chirwere.

mabatiro

Mastocytosis chirwere muvana. Its zvinokonzera kuti nepose vakatsunga. Ndiyo nguva kutanga kurapwa. Dzinenge nzira vasati vasikwa. Kuvandudza mamiriro mwana rinoshandiswa symptomatic kurapa. Vavariro kurapwa - kuderedza basa pedanda rechikepe sero kukura. nendumure Older nevana ushandiswe:

  • Zvinodhaka pamusoro Kurwara: "Suprastin", "Tavegil" uye vamwe.
  • Mishonga inokwanisa pakudzikamisa kushanda masero kwakaipa.
  • PUVA mushonga. Kuonekwa ganda pamwe ultraviolet chiedza. Zvichatora maviri nemashanu muzvirongwa. Rinoshandiswa nenzira chiitiko kuti antihistamines regai nezvibereko. Nzira kunobatsira kuderedza uwandu makwapa paganda.
  • Cytotoxic yomuchipatara (systemic chimiro chirwere). The chirwere navo kwete mushonga, asi kuti anonoke pasi uye vanorega ikure mafuta masero sezvataigona.

Tsvagurudza chinokonzera mastocytosis muvana, kurapwa mune zvimwe zviitiko, kunogona kuitwa vachishandisa tsika mushonga Quick.

Treatment acho nzira

Pakarepo kuyambira, ndeyokubvisa chirwere nenzira iyi zvinogoneka chete pashure zano nachiremba wako. Plants anobatsira kuderedza kuvaviwa uye akashatirwa ganda. A shoma Recipes:

  • Dzekorianderi (miriwo upfu) yakavhenganiswa weupfu shuga iri nhamba mumwe munhu. Shandisa hafu yetea pamberi kudya.
  • Aizomupa Ivy. Yetea kuti mioak omuti ndinoiitawo Ivy mashizha dira kufashaira mvura (imwe fő), uye kusimbirira kuti zvichitonhorera. It anoita tsonyera. The pachena nzvimbo akabata maminitsi makumi maviri.
  • The aizomupa yorukato. Tora rimwe spoon kuti yorukato akaomeswa. Akadurura girazi yakabikwa mvura. Zvomoto nzvimbo vakachenesa iyi mhinduro kakawanda pazuva.
  • Mastocytosis muvana ikarapwa zvakawanda mishonga dzokugezera. Kana kugeza mu vodichku akawedzera: chamomil, celandine, yorukato, somuzivi uye dzakatevedzana.

Kushandisa Nzira idzi kubvisa zvachose mwana asingagoni dambudziko, asi yake ezvinhu zvakanaka.

Zvakaipira chirwere

Kakawanda nyaya yose akadzokorora: vaicherechedza mapundu pamusoro mutumbi mwana, pakarepo kubata chiremba wako. Mushure zvachose chisingakuvadzi chirwere mberi kune dambudziko ihombe: kukuvara nhengo uye rufu.

Fungidziro chirwere kunoenderana mhaka mastocytosis muvana. Mufananidzo rinoratidza kuti matambudziko kazhinji voga uye muviri wemwana hausi kunyange mavara.

mhedziso kwakadaro kunogona kuitwa kuti systemic lesion. Kana rechikepe sero neleukemia kunokwanisa kuonekwa, hazvina zvakakodzera kutaura pamusoro zvakanaka kukura. Ndicho chikonzero tikapfuudza zvakare: regai sungisa pamwe nokurapwa. Pakarepo kubata chiremba wako.

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