Turner kuti urwere

Shershevskii-Turner chirwere ari chromosomal chirwere, icho pamwe chete dzakananga abnormalities mu kwomuviri. Kunogona kuita kuti kurara infantilism.

Hosha paakarondedzerwa muna 1925. Zita rokukudza chiremba (N. A. Shereshevskogo), vakasvika kuna rondedzero iyi. Muna 1938, Turner chaiitirwa zvokuwedzera, iyo yakabatsira kusimbisa vanamwari vatatu vatatu zviratidzo zviri chirwere. Vamwe zvezviratidzo izvi yakarondedzerwa dzepabonde infantilism, ari deformation pakati kugokora mapfundo, bapiro ganda pazvirugu kuti kuitika mumutsipa.

chirwere Turner vake, husingaoneki izvo zvinogona kuwanika paIndaneti, achiri inoshamisa chirwere, sezvo haripi chaiyo zvikonzero chitarisiko chake. Chiripo chete kuti chitarisiko chake kunokonzerwa sei nepamuviri uye pakusununguka. Underdeveloped gonads mune vanhu vane chirwere ichi vari akatsanangura zvepabonde chromosome kuremara.

Turner urwere: Zviratidzo

In embryo, kazhinji zviri utachiona mumasero hakuna abnormality, nhamba wakarurama. In yechipiri yezana pamuviri, unogona anoiona dzichimhanya involution, kureva, zvakasiyana kukura. Pakazosvika nguva panowanikwa nhamba kuzvarwa muna ovary mamota pazasi dzose. Mune zvimwe zviitiko vanotoda vasipo. Zvinoguma raidudzwa kushayikwa mukadzi bonde mahormone, anogona kucherechedza pabonde zviratidzo underdevelopment. Zvinenge varwere vose chirwere ichi vari mbereko.

Chromosomal kuchinja kukonzera malformations siyana. Pamusoro pokumuka urema izvi kukanganisa uye anoenderana kunotouraya.

Gonads mune chirwere ichi vari undifferentiated connective tambo zvisingakwanisi ane zvinhu gonads. Ndoda anogona kusangana pezvokuvamba testes uye ovaries zvokuvamba. Uyewo, pane kushoma zviitiko zvinoita kuchengeta pedzidziso dzekutanga vas deferens.

Turner chirwere kunoguma kuchinja mapfupa uye mapfundo: minwe, tsoka, maoko vari kutapudzwa, chiningoningo vadyi iri akaremara vertebrae akawisa.

The chirwere chinogona kukonzera mwoyo chirwere, itsvo uye nemidziyo makuru. A maitiro chepfungwa chirwere - ganda matanga kumativi mumutsipa.

Varwere vari lagging mumashure kukura kubva pakuberekwa. Neonates ungacherechedza zvakawandisa ganda pamutsipa, yakayamwa dzepanguva, kazhinji kuputswa, kazhinji vomits uye regurgitation kunoitika tsime.

Kuwedzera zvarakasiya vakachengeta kutsauka mu mupfungwa kukura kwomuviri. In tsinga pane nguva dzose pamusoro zvokurwara zvimwe mhando.

Turner urwere anoita vanhu kukakanganiswa. Ivo Kashoma kukura kupfuura hafu mita. Muviri uremu nenguva wandisa.

Sexual underdevelopment iri, muchiitiko ichi, zvikuru, chaiyo chaizvo. Kazhinji munhu anogona kuchengeta geroderma uye yokubereka labia majora vanogona kuva moshonkovy atarire nyinyo suo anova Wavy, labia kazhinji underdeveloped.

Ko underdeveloped uye mazamu, minyatso dzinenge nguva dzose yakaderera. Unogona uone uterine hypoplasia.

Turner kuti chirwere haisi kwazvo simba pfungwa, asi zvinokwanisika kuchengeta yokufara infantilism.

Kuongorora chirwere uye kurapwa

Hwaro nechirwere anowanzoramba zvekuchipatara zvinhu. Dzimwe nechirwere bvunzo ropa.

Treatment anogara refu. In wokutanga Danho rose simba raunoda kupedza pane chinhu havi kukura. Kuti aite izvi, kushandisa anabolic steroids uye zvinodhaka. In ichi chinokosha chenguva gynecological kuzvidzora.

The chikuru kurapwa estrogenizatsiya. Muperekedzei inogona gumi chete. Treatment inoenda ndechokuti muviri, uyewo yechipiri zvepabonde maitiro dzinotanga kukura.

On upenyu fungidziro akanaka chaizvo. The chete kunze vari varwere mwoyo chirwere. Early kurapwa pamwe mahormone kunogona kubatsira kukurira kushaya mbereko.