UtanoMushonga

Ataxia - chii ichi? Zviratidzo uye mhando ataxia

Ataxia - haina achiperekedzwa nourema dysmotility, ndiyo maitiro zvinhu mutinhimira zvirwere uye motokari Kufambisa. Rinoshandurwa kubva pane rechiGiriki rokuti ataxia rinoreva "nyonganyonga" uye "kuvhiringidzika".

With ichi chirwere kufamba kuva disproportionate, vachinyara, kururama, kazhinji chirwere kufamba, uye mune zvimwe zviitiko kunyange kutaura. Chimbofunga nemhando ataxia kumira uye chii maitiro avo.

Friedreich kuti ataxia

Friedreich kwakaita ataxia - a majini akaita chetsinga chirwere, iyo unobereka kunoramba hunhu. The kutanga zvinoratidza chirwere kuva pachena yokutanga shoma emakore oupenyu.

Chokutanga, pane kutyorwa manyorero uye gait. Nokuti vana Zvisinei, zvinoratidza kutyorwa manyorero kwakaoma nokuti kuti haisati yanyatsosvika kuumbwa. Maererano gait, murwere uyu nyaya anofanira kutsigira, akaramba swinging. All kufamba makumbo zvakawanda jerky kupfuura mberi.

Inokudziridza pamusoro nguva nekusagona kumira (astasia) uye kunyange kufamba (Abaza). Zvisinei, yokupedzisira chaiwo aratidze nokukurumidza mberi nzira chirwere uye nzendo ayo okupedzisira.

Vaichengeta zvachinja nomuzongoza, chiri kunyanya kukosha kuyaruka, umo gadziriro yayo inotungamirwa ichigere kupera asi. Kwapera makore mashomanana murwere nemhaka yezvikanganiso mubasa rwatata kuva chirwere cheshuga. Papera chinguva nemhaka chinopedza kuchinja gonads kunoitika hypogonadism. In yokupedzisira nzendo ataxia anobatana zvinoona vachivavhiringidza yomuka somugumisiro chinopedza zvachinja optic uye oculomotor tsinga. Pamusoro paizvozvo, wakakodzera kukanganisa kune Tutsinga tunofambisa mashoko utwu muuropi hwapedyo dementia.

The kukundwa of cerebellum

Cerebellar ataxia - kukanganisika gwenya kufambisa, kukura pamwe kukundwa huru kubereka basa nokuti, muviri - pfungwa cerebellum. Mune zvimwe zviitiko yakatanga duku kuchinja, uye mune dzimwe - zvikuru uye rinorema.

Kukura ataxia kwakadaro kunoitika maonero inobatanidza nzvimbo dzakasiyana pamusoro cerebellum pathological muitiro. Kazhinji cerebellar ataxia nechirwere encephalitis, cerebellar vascular zvirwere, multiple sclerosis, akaipa uropi namamota, chepfu, uye zvimwe zvirwere zviri magene mavambo. Govera 2 Mhando cerebellar ataxia - kunofambira mberi uye simba.

The kunofambira mberi nature cerebellar ataxia

Cerebellar ataxia yakaratidzwa kunofambira mberi maonero rutapudzo kuti tsandanyama matauriro. Murwere pakuitika zvinova zvakaoma kwenguva refu kugara imwe nzvimbo, sezvo akanga zviduku kutyorwa motokari Kufambisa. Man runoita yakakura chaizvo uye hwakasiyana matanho akaita iri ezvinhu kudhaka. In Muzviitiko zvakaipisisa, murwere chirwere haisi kukwanisa kugara uye kumira, nekuti vasina simba kunyange kubata musoro wake, iye anogara pakugumburwa. Kunofambira mberi ataxia kwazvo kuwana murwere anogona kuramba kuenzanisa pachavo. Zvinokosha kucherechedza kuti pane chinonzi motor Kufambisa hazvirevi kukanganisa chii ane mwoyo murefu rakazaruka kana maziso.

The simba nature cerebellar ataxia

Amyotaxy hunovapo nezvokupindira iri cerebellar hemispheres iri pathological muitiro. Kana-siyana chirwere Kufambisa zvinetso zviri vakachengeta chete apo zvinhu kufamba. Kurasika kumeso uye chaiwo kufamba, vari kutsvaira uye zveufende. Discoordination uye tava kuderera nemafambiro musi njodzi divi. For simba ataxia kunoratidzwa hypermetric (kunyanyisa, anoshorana motokari) adiadohokinez, promahivanie uye chinangwa tremor uye kutaura zvinetso (varwere Taura seiyi nokutyora mashoko kupinda mabhii).

Muna amire uye achifamba murwere vakatsauka mune tsamba dzaparadzwa cerebellar hemisphere divi. Anochinja murwere manyorero: zvinova mafungu, vakashinga, guru tsamba. Zvinokwanisika rutapudzo kuti mudzira hunenge.

kutsinga dzinouya ataxia

ataxia ichi - kukanganisika sangano, umo kuchinja gait kunoitika nokuda kurasikirwa manzwiro ari makumbo, inova migumisiro peripheral tsinga, medial loop, nembiru undovakira uye posterior Midzi musana. Murwere haadi kunzwa nzvimbo makumbo, uye saka arikutadza zvose kana achifamba uye kana yakamira. Kazhinji, akamira namakumbo paupamhi voga uye panguva imwe chete inogona kuramba takatsiga chete nemaziso yakazaruka, asi kana ivo kuvhara, ipapo munhu anotanga vachidzungaira uye chinowanzoitika kuwira (zvakanaka chiratidzo Romberg). Kana achifamba, varwere uyewo straddle uye muvatakure dzakakwirira zvikuru kupfuura zvakafanira, uye asina kuzvironga swinging nayo nokuku. tsoka dzavo akasiyana urefu, uye tsoka kugunzva pasi, kubudisa mukakachurwa mitinhimira. Murwere anofamba ichiita anoshandisa tsvimbo rutsigiro uye vashoma Bends ari muhudyu majoini mutumbi. Gait chainetsa sembura ziso zvikanganiso. Varwere kazhinji vasava isimbe, famba uye kuwa kana kugeza chiso chako, sezvo iye maziso ake, vanorasikirwa nguva kuona kuzvidzora.

spinocerebellar ataxia

Iri izwi rinoreva munhu muzvizhinji kuti injini zvirwere anomuka zvikurukuru nokuda ischemic CNS kukuvara kana perinatal hypoxia. Kuchinyanya muupenyu gait angava akasiyana uye zvinoenderana kwokuomerwa uye yezvakaita lesion. Saka, chiedza anogona kukonzera kukuvara zvishoma Babinski, wakawedzera mudzira hunenge, uye kwete achiperekedzwa anyatsoona nokuchinja gait. maronda akakura uye zvikuru kazhinji kunotoreva mativi hemiparesis. Kuchinja kuitika uye kiyi gait noruzhinji paraparesis.

Palsy zvinowanisa kufamba zvirwere kunotoreva kuchinja gait. Varwere saka pane involuntary fambisa maoko nemakumbo, ayo achiperekedzwa grimaces pachiso kana mutsipa kutenderera masangano. Kazhinji, makumbo rakawedzera uye maoko hwakakungwa, asi ichi muzvidimbu asymmetry ave pachena chete mushure nokunyatsocherechedza murwere. Somuenzaniso, mumwe ruoko inogona kuwedzerwa uye pronated nevamwe supinated uye flexed. The asymmetric nzvimbo yayo uye rinowanzoberekera kana akatendeuka musoro wako kwakasiyana-siyana.

kuongorora chirwere kuti ataxia

Nokuti chirwere kushandisa chirwere mitoo yakadai se:

  • MRI uropi;
  • pfungwa electroencephalography;
  • DNA Diagnostics;
  • electromyography.

Kuwedzera chero ataurwa nzira zvakafanira kuti bvunzo ropa, kuti ndiongororwe vanachiremba akadai wetsinga, chiremba wepfungwa uye ophthalmologist.

ataxia kurapwa

Ataxia - chirwere chakakomba kuti inoda yakakodzera chiito. Treatment iyo anoitisa nyanzvi wetsinga, zvinganaka ndiyo symptomatic uye inosanganisira zvinotevera.

  1. kurapa rokudzorera (anticholinesterases, "cere the" ATP, B mavhitaminzi).
  2. Physical kurapa zvainanga wokudzivisa siyana yematambudziko (atrophy uye tsandanyama contractures Somuenzaniso) Kusimudzira kufamba uye co-kugadzwa, kuramba chaiko kugwinya.

Special yokurovedza muviri yakaoma muviri muviri kurapa, chinangwa chiri kuderedza incoordination uye achisimbisa netsandanyama. Kana nzira yakakura kurapwa (kuvhiyiwa cerebellar namamota, somuenzaniso) inogona kutarisirwa zvishomanana kana zvakakwana kupora kana kanenge kurega zvimwe kunoita.

In Friedreich kuti ataxia, kufungisisa pathogenesis kwechirwere chacho, unogona kuridza chihombe basa zvinodhaka zvainanga kuramba mitochondrial nerevane ( "Riboflavin", vhitamini E, coenzyme Q10, succinic acid).

The fungidziro chirwere

Kufembera enhaka zvirwere rakanyatsojeka zvisingafadzi.. Over nguva, kunyanya kana zviri simbe, neuropsychiatric zvirwere chete mberi. Vanhu vane chirwere kuti "ataxia", zviratidzo izvo nezera kuva raidudzwa, sezvo mutemo, akaderedza zvikuru kukwanisa kushanda.

Zvisinei, nokuda symptomatic kurapwa, uyewo kudzivirira kudhaka, kukuvara uye zvirwere, varwere akakwegura.

dziviriro

Kutora matanho zvakananga ataxia hazviiti. Chokutanga, hazvina kunodiwa kudzivisa zvichibvira chidzoke uye kukura chakakomba zvirwere (sinusitis, otitis, mabayo, semuenzaniso) anokwanisa unotokonya ataxia.

Zvakakosha kudzivisa michato ropa. Uyezve, tinofanira kuyeuka kuti ndingangokuvara kupararira enhaka ataxia kubva mubereki mwana, uye nekuti varwere kazhinji zano kumisa nokuberekwa kuvana vavo uye kuti vave womumwe mwana.

Ataxia - chakakomba chetsinga nyonganyonga, kuti izvo unoda kutanga kurapwa pakarepo. Ndicho chikonzero nokukurumidza chirwere ichi vave kuzivikanwa, nani kuti murwere kuti ramangwana.

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