The anomaly Arnold Chiari Type 1 - chii? Zviratidzo, migumisiro, kurapa

Hapana chakavanzika kuti panguva paumbwe embryo ari mudumbu raamai ave zvokurwara siyana kusanganisira anomaly Arnold Chiari mhando 1. Chii chinonzi chirwere ichi? Doctors vanodana Fani iyi kurambwa kuti ikabuda iri mudumbu nokuda mismatch iri kukura dehenya uye pfungwa, dzakagara mariri. Tiri kutaura nzvimbo uko cerebellum. Zvinoguma iya iri repamusoro chikamu nomuzongoza tonsils akaparadzaniswa mimwe kukanganisa.

zvinokonzera

Anogona zvinoitika vanhu kuvapo, kana iri dzakaonekwa anomaly Arnold Chiari mhando 1? Life anotarisirwa, vanoti vanachiremba, runotsamira zvinoverengeka on: mwero uye chimiro chirwere. Usati akaisa chokupedzisira nechirwere, ivo kusarudza zvinokonzera zvakazoita kuti kukura variations:

1. Vachiberekwa. More mu utero fetus dehenya deformation kunoitika: fossa iri muna cerebellum, hapandiringani kukura uye kukura pfumbu nyaya. Zvimwewo vachiberekwa zvikonzero akanyorwapo simba kuwedzera foramen kuti mudumbu panguva paumbwe marangwanda.
2. Yakatengwa. Chokutanga munhu achimukuvadza musoro panguva pakuzvarwa. Uyewo muchikwata ichi vari musana kukuvara: inokanganisa ake doro - chaiyo mvura, panowanikwa hydrocephalus nezvimwe musana abnormalities.

Kuti kuva kumbotenderera, chaiwo zvikonzero masayendisiti haagoni asi kudana. Chinhu choga vava nechokwadi chokuti chirwere hauna chokuita chromosomal abnormalities.

zvinokonzera njodzi

Munhu wose anoziva kuti panguva trimester pamuviri rokutanga, fetus anoenda Tab kusvika zvose nhengo. Naizvozvo, nzira yakarurama woupenyu mai inokosha kwazvo chakaipa kukura mwana. Kana mukadzi asingafukidzi zvinoenderana dzinokosha anobata ramangwana ichi hunokonzera yakawanda yematambudziko. Kana Chiari urwere, mukana parinowanika iri yakawedzera zvinhu zvinotevera:

• Bad Miitiro mai: kusvuta, doro uye kushandisa zvinodhaka.
• Kushandiswa simba zvinodhaka, dzokuzvirapa.
• Kutamiswa zvirwere zvinokonzerwa nemavhairasi, kunyanya gwirikwiti.

At zvikuru chiedza siyana chirwere akaberekwa mwana haafungi kusvikira pakuguma upenyu anokosha zviratidzo, kunyanya kana iri panoonekwa anomaly Arnold Chiari mhando 1. Vana vangani kurarama, vane rechitatu kana kuti rechina pavaipfuura chirwere kunyange? Doctors kupa mwoyo Zvaifungidzirwa. Zvinosuruvarisa zvakadai kazhinji, nendumure zvinofanira rufu. Kunyange kana mwana ari kutanga zvaimirirwa chirwere rechipiri kana akawanikwa, anofanira kurapwa: kuvhiyiwa, asi kushanda ndiyo 85%.

urwere mhando

Pasinei kwayo zvakaoma kwazvo, vari vose chokuita pasi kwazvo nzvimbo cerebellum. The kwakadzama uye zvakawanda amygdala pasi mukati musana canal, ine ngozi zvikuru uye nezvimwewo zvirwere: naye rokuongorora uye dzimwe abnormalities. Zvichienderana ichi uye kupa 4 nezvimiro zvokurwara:

1. The anomaly Arnold Chiari Type 1 - chii chirwere chakadai? Kazhinji haakonzeri zvimwe zvinetso kukura kwemwana. Structural kuchinja muuropi hariwanikwi, ivo tonsils dziri munzvimbo remuromo nharaunda.
2. chechipiri mhando syndrome. Cerebellum aoma zvakachinja kupinda foramen magnum, panguva imwe chete pane Muviri siyana abnormalities nomuzongoza, uropi uye musana.
3. The chirwere ndiyo mhando rechitatu. Nemamiriro of hindbrain iri zvava kusvika foramen magnum zvachose. heniya achiumbwa mapazi ichi.
4. Arnold Chiari chirwere ndicho mhando wechina. It kunoratidzwa cerebellar hypoplasia - ayo underdevelopment. Zvisinei, haana kufamba uye runowanzotaurwa nezvarwo hydrocephalus uye vachiberekwa cysts ari posterior cranial fossa.

Vanachiremba vanoti kuramba 2nd, 3rd uye 4th mhando kazhinji chirwere akabatana nevamwe vakaremara yakanyanya kukura mwana: heterotopia pakati cerebral cortex, subcortical zvivako hypoplasia, abnormalities ari corpus callosum , uye zvichingodaro.

Huru Zviratidzo

Sezvambotaurwa, kana padariro hosha iri chiedza chaizvo, uye uropi akabata zvishoma, chirwere chinogona kuitika zvinenge zvose hwake, pasina kukanganisa munhu. Asi ichi ndicho isingawanzowanikwi mhosva. Kazhinji zvachose uye nguva nomusoro - huru chiratidzo chirwere ichi ndiyo anomaly Arnold Chiari mhando 1. Zviratidzo nzira iyi migraine kunze izvi: kurwadziwa pamutsipa, tinnitus, kuda kurutsa uye kurutsa, neutera maoko, aikanganiswa yokurasikirwa maoko nemakumbo, pamberi kuona uye chiono kaviri, isingagari gait, kunokanganisika matauriro, uye unonetseka pakufema.

Maererano chirwere ari mhando rechipiri, iri ngozi zvikuru uye kwakatooma, ayo anozivikanwa zviratidzo kuonekwa huchangogadzwa kana pane muduku chaizvo (kakawanda kuenda kukireshi). Kazhinji wheezing ndiyo kufema noruzha mu vacheche, simba rokuchema, kufema uye kumedza. vachangoberekwa kwakadaro pakarepo azopora uye vari kuedza kuponesa kuburikidza kuvhiyiwa. Muzviitiko izvi, chinhu chikuru - musapotse nguva kana uchiri kukwanisa kuponesa upenyu hwemwana.

zvimwe zviratidzo

Ivo kuchengetwa zvikuru madhigirii yacho syndrome. kazhinji Primary manyuko myocardial uropi kana musana tiri zviratidzo anomalies Arnold Chiari 1 mhando hakusi chaityisa zvokuti ake mamwe subspecies. Ivo dzinoratidzwa kwete chete zvakaratidzwa kaviri, asi upofu wakakwana, kurasikirwa pfungwa, kurasikirwa kufambisa, chakamira pakunodengenyeka zvine pakati wamativi, nezvinetso weti, tsandanyama simba, kurasikirwa manzwiro guru chikamu muviri (dzimwe nguva yose hafu muviri).

Development dzakasiyana utano migumisiro angaita chinhu anomaly Arnold Chiari mhando 1. Life anotarisirwa uye zvarakanga kosi kuvimba nokukurumidza uye yakarurama kuongorora chirwere. Nzira chete kuona zvokurwara chiri MRI (rinobva resonance kuri) wouropi. Zvinoda murwere ezvinhu kutadza kufamba zvakakwana, saka vanoshingaira vanozvarwa euthanized pamwe mishonga inokosha. Achibatsirwa mudziyo uyu dziri achiongorora nomuzongoza, musana, remuromo uye thoracal marangwanda. MRI anogona kuziva kwete chete urwere, asi vose pathologies pematanho chirwere.

yematambudziko

Kugadzirwa pathologies siyana vanotsamwisa anomaly Arnold Chiari mhando 1. Migumisiro zvinogona akasiyana chaizvo: nekuora arachnoiditis uye anopera parenchymal maronda ari axon. Kunyanya zvakajeka yematambudziko izvi zvichiitika tikafunga kweropa zvirwere zviri etsinga dzomuviri. Neuropsychiatric zvinetso, muchiitiko ichi kuonekwa kwapera uye kuedzwawo muchimiro sokunonoka kukura paraplegia. Kana anomaly iri kukura chaizvo zvishoma, inotungamirira hydrocephalus - kunyanya kuunganidza mvura iri ventricular ezvinhu uropi.

Uyezve, Arnold Chiari chirwere kunogona kukonzera compression simba vakadaro musana kuti munhu zvakakwana mitezo. Under zvayo inokanganisa vanowanzotanga kuumbika cysts uye in vari nomuzongoza, vanogashira mvura kuti anovhunanya musana basa. Zvinogonekawo yematambudziko pamwe kufema kusvikira anomira. Dzimwe nguva vanachiremba yakanyorwa varwere congestive nemabayo - inova migumisiro nezvokuti munhu anorasikirwa kukwanisa kufamba akasununguka.

kuchinja mabatiro

The chirwere ari kubatwa nzira mbiri. Vanachiremba vakasarudzwa kuchinja kana kuvhiya nzira zvichienderana zviratidzo uye zviratidzo wakaratidzwa murwere, kwokuomerwa evanhu, zvakaoma kunzwisisa uye nemigumisiro chirwere. Dzimwe nguva chete zvinodhaka vangarwisa zvirwere zvakadai Arnold Chiari mhando 1 anomaly. Imhandoi kurapa? Chokutanga, chiremba anoramba anoitisa purogiramu inspections murwere, anoritungamirira kuti Consultancy vakasiyana nezvokurara, uyo pashure zvakakodzera kubvunza anofanira kutora matanho akakodzera.

Kana murwere anonyunyuta kurwadziwa munzvimbo occipital munzvimbo musoro kana pamutsipa, iye ushandiswe inonyaradza marwadzo omusoro uye Anti-anogumbura vamiririri, uyewo mishonga inobatsira kwenyama dzemuviri. Zvinobatsira chaizvo uye chinokosha kuchirapa muviri - chiitwa zvainanga kubvisa nokudedera maoko nemakumbo, uye normalization kuti Kufambisa. Zvinangwa izvi, sezvakarayirwa chinoshingaira Occupational kurapa. Uye zvimwe zvichaita kubatsira namazvikokota chiremba wechikadzi achindidzidzisa kutaura, ndiani achakwanisa kubvisa matambudziko nokutaura. Nzira dzose idzi kunogona kunonotsa kana kudzivirira zvachose pakutapirwa kubva zvoutsinye kurapwa - kuvhiyiwa.

kuvhiya kupindira

Zvinoitika kuti apa matanho regai kubatsira - vachishingaira anoramba kuumba uye kununura boka dzichikunetsa Arnold Chiari mhando 1 anomaly. Treatment ipapo Kuchinja zvinoshamisa: chiremba anotanga kugadzirira munhu kunorapwa. Neurosurgical mashandiro ari kuitwa pamwe matatu kunangwa. Chokutanga, kubvisa zviratidzo zvakakura zvakadai nehosha, akadai kurasikirwa pfungwa, ziso nenyonganiso, tsandanyama simba. Chechipiri, kupindira kunobatsira kubvisa anyatsoona zviratidzo - kubvisa compression wouropi. Chechitatu, achishandisa kuvhiyiwa zvinoguma mwero kufamba nezvinobata.

Kupindira unorembedza muitiro zvachinja nemamiriro musana uye ndachena nyaya: somugumisiro zviratidzo kuserera, murwere anotanga kunzwa zviri nani. Kazhinji, vanachiremba kubva rwemberi akabvisa cranial fossa mapfupa chomudziyo: nzvimbo kunowedzera uropi, wachena nyaya hunoguma kuti misha uye kusvinwa. Uyewo kunoderedza intracranial nevezera. Uyezve, vanachiremba zviri kushingaira kushandisa mitoo yakadai kusonanidzwa uye pakazovharwa musana mugero.

dziviriro

Kuti mwana haana kuva pamusoro matambudziko, amai vanepamuviri vanofanira kukoshesa munzvimbo dzavo. Chekutanga, inofanira kuongorora zvose zvinogoneka abnormalities kuti munguva mudumbu: malformations ari Neural chubhu, Down kwakaita Syndrome, Arnold Chiari mhando 1 anomaly. Chii chirwere ichi, sei zvaitika, uye matanho api anogona kutorwa kuderedza ngozi izvi nezvimwewo abnormalities, vanofanira kuziva mai ose pamuviri. mukadzi nomazvo uye anoziva pamuviri vachava zvinogoneka kudzivisa zvose zvinhu zvine inokanganisa paumbwe embryo.

Chechipiri, mukadzi anosungirwa zvakazara kudya, kudya zvakasiyana siyana zvokudya utano: hove, nyama, michero, miriwo, zviyo nezvinogadzirwa nomukaka. Zvinonzi zvakasimba kutendera doro. Uyewo, unofanira kurega kusvuta, tisingatauri zvinodhaka uye zvinodhaka zvakasimba. mishonga ipi, kunyange Homeopathic, amai vanepamuviri kunotora chete pashure yachiremba mushonga. Chechitatu, mukadzi ane zvakawanda kufamba, kufema mhepo yakachena, kuenda chaizvo. About tsinga, manzwiro uye rekusuwa ndiko kuti kukanganwa, kunakidzwa chinzvimbo chake uye rinyatsomubatsira mufaro muupenyu.