Utano, Zvirwere uye Conditions
Caroli nehosha: Zviratidzo neMarapirwo
chirwere Caroli ndiro zvikuru kunzwisisa dzichipfekeka rikavapo pamusoro pechiropa, chirwere uye kurapwa hunokonzera zvinetso zvakakomba kuti vanachiremba.
Chii chinonzi chirwere
marudzi chirwere
To musi, yakazvimirira kupatsanura pakati Caroli nehosha mune mushonga chisipo. Zvisinei, pasinei neizvi, kune mbiri dzakasiyana siyana chirwere. The chimiro chokutanga kunoratidzwa muna kuti yakaputsika biliary patency, pamwe haizopereri inotungamirwa yematombo.
Advanced bile ducts anogona chokuita nzvimbo cystic chiropa uye nokudaro mufanidziro partition rusvingo thickening mu chikofu lumen.
zvinokonzera
Mune zvimwe zviitiko, hosha iri tuhova pathological kusagadzikana chiropa, iyo zvinoomesa zvikuru kurapwa.
Huru Zviratidzo
Caroli nehosha zviratidzo vanogona kuratidza pachavo vari zvachose chero zera muvana uye vechidiki. Zvinokwanisika kutakura chikuru zviri chirwere akadai:
- abdominal kurwadziwa;
- fivhiri;
- zvishomanana yellowness ganda;
- chiropa akawedzera pamusoro palpation.
SERVICING iri
Pasinei chokwadi kuti zviratidzo hosha zvakakwana akaratidza, asi zviri uyewo maitiro mamwe akawanda chiropa zvirwere. kuongororwa zvakarurama uye kuziva zvirwere zvinogona Caroli ari US uye panguva CT. Computed tomography ichaongororwa chimwe chezvinhu anodzidzisa nzira kuongororwa, nekuti unogona kuona zvakanaka zvakakwana ose kutyorwa nemitemo. Uyezve, endoscopic cholangiography kungadiwa kuti chirwere.
Chiropa basa nemiedzo kwenguva refu Zvisinei kuchinja, pamwe kuchiita chirwere uye refu kushoma munyika nokukanganisika kuongorora ropa anogona kuziva zvose nezviratidzo cholestasis.
Features kurapwa
In pamberi Caroli chirwere kurapwa nhungamiro inofanira kuchengetwa haambokundikani, nekuti zvokurwara iri mberi zvakasikwa. Treatment zvinoreva kubudikidza nokushandisa mishonga inorwisa mabhakitiriya, uye ursodeoxycholic iine acid Kutarisirwa mamiriro kudzivirira calculus inotungamirwa.
Mukuwedzera, kurapwa unotora:
- analgesics;
- litholysis mabwe;
- biliary abudise.
Pamusoro accession, cholangitis, kana zvimwe matambudziko anoitika purulent mishonga hapana vakasiyana kurapwa kwemabhakitiriya cholangitis. Zvakakosha kuti kubvisa urwa uye ipapo yokunatswa rinoitwa kubva bile mutsinga dzinofamba nemukaka, uye vakashandisa mishonga kubatsira kubvisa chirwere.
Kana simba kwazvo kuwedzera ndima uye biliary bile kurega kunotanga, chiremba anogona kuitisa kubviswa imwe akafukidza chiropa. In Muzviitiko zvakaipisisa, hepatic insufficiency pamberi kana zviratidzo degeneration ari akaipa bundu, chiropa anogona varumbidzwa kubva yepedyo.
Nokuti migumisiro yakanakisisa, vanachiremba vakawanda dzinorumbidza tikapedza chiropa transplantation kunyange kusavapo kwazvo zviratidzo zviri kutanga nzendo chirwere. Zvisinei, kazhinji, kuvapo chirwere chinhu contraindication kuti transplantation. Varwere wokurarama pashure transplantation pamwe vachiberekwa fibrosis kuti vave anowedzera chirwere cholangitis panguva transplantation, iri nani pasi.
Fungidziro chirwere ichi zvikuru vanoshorwa, sezvo zvazvo kunogona kuitika pamusoro akawanda. Zvisinei, zvikuru kashoma zvinoguma rufu murwere.
Caroli chirwere
Disease Caroli kazhinji chokuita vachiberekwa hepatic fibrosis, zvichiguma ane Caroli chirwere. Vaviri pathologies idzi inoumbwa ne rinenge kufanana chimiro biliary zvinetso zviri chiropa rinenge pachiyero embryo kukura. The chirwere iri nhaka yepedyo uye hwakaratidzwa abdominal marwadzo uye nekudeura ropa kubva esophageal varices. Neonates angava mubatanidzwa huru zviratidzo vachiberekwa hepatic fibrosis, Caroli chirwere uye polycystic cheitsvo.
chirwere ichi zvinoreva vachiberekwa bile mutsinga dzinofamba nemukaka chikofu Zvisinei, kashoma zvikuru uye zvikurukuru vanhu vane makore pasi pemakore 30. Mumakore mashoma makore zvokurwara okutanga kunoitika zvachose asymptomatic, sokuvapo pakuwedzera bile ducts musanetsa kurega kunotanga kubva bile, izvo achasika ezvinhu kuti paumbwe mabwe accession hweHIV. Kana kushandiswa pamwe nevamwe akaona zviratidzo jaundice, inoratidza kuvapo cholangitis.
It vakapemberera kunyanya kuruboshwe madziro kukuvara chiropa, asi rinogonawo kuva maviri-nzira dzimwe nguva.
Mune zvimwe zviitiko, chiropa chakasimba zvokuti rinogona kukanganisa dzimwe nhengo. Saka rimwe yematambudziko anogona kunzi sezvo panowanikwa renal kukundikana.
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