UtanoZvirwere uye Conditions

Caroli nehosha: Zviratidzo neMarapirwo

chirwere Caroli ndiro zvikuru kunzwisisa dzichipfekeka rikavapo pamusoro pechiropa, chirwere uye kurapwa hunokonzera zvinetso zvakakomba kuti vanachiremba.

Chii chinonzi chirwere

Caroli Disease - zvisingawanzoitiki vachiberekwa chiropa chirwere kunokonzerwa pakuwedzera bile ducts, iri mukati mumuviri. It kunoratidzwa muna kuti inowanzotorwa motokari iri kwakakanganiswa bile kurega kunotanga kunoitika uye ayo accession hweHIV. Kazhinji chirwere kwakakurumbira nevanhu, uye kuchitanga pauduku kana kuyaruka. Kufambira mberi pathological kwacho kunobva mari uye mwero kuvadza ducts mukati chiropa.

marudzi chirwere

To musi, yakazvimirira kupatsanura pakati Caroli nehosha mune mushonga chisipo. Zvisinei, pasinei neizvi, kune mbiri dzakasiyana siyana chirwere. The chimiro chokutanga kunoratidzwa muna kuti yakaputsika biliary patency, pamwe haizopereri inotungamirwa yematombo.

Chechipiri chimiro chokuita vachiberekwa hepatic fibrosis. Muchiitiko chino, pane zvishomanana rokuwedzera ducts uye paumbwe mabwe kunobvira, kunyange zvazvo dzimwe nguva dzinoitika akazotevera nzendo chirwere.

Advanced bile ducts anogona chokuita nzvimbo cystic chiropa uye nokudaro mufanidziro partition rusvingo thickening mu chikofu lumen.

zvinokonzera

Caroli chirwere zvinoreva vachiberekwa zvirwere anomuka nokuda imwe autosomal recessive kwadzinoita nhaka. Kana uine pedyo nehama pamwe akafanana zvokurwara, pashure pakaberekwa mwana pakarepo vanofanirawo kuitisa misoro kuongororwa, sezvo kunonyanya mukana dzokupfuudzira enhaka zvirwere.

Mune zvimwe zviitiko, hosha iri tuhova pathological kusagadzikana chiropa, iyo zvinoomesa zvikuru kurapwa.

Huru Zviratidzo

Caroli nehosha zviratidzo vanogona kuratidza pachavo vari zvachose chero zera muvana uye vechidiki. Zvinokwanisika kutakura chikuru zviri chirwere akadai:

  • abdominal kurwadziwa;
  • fivhiri;
  • zvishomanana yellowness ganda;
  • chiropa akawedzera pamusoro palpation.

Kunoonekwa kuratidzwa kurapwa chirwere zvinowanzobatanidzwa panowanikwa chokutsva. Kumboda Caroli hosha chirwere mukono vana. Panguva exacerbation rave unopinza kuwedzera padanho bilirubin uye machena eropa count.

SERVICING iri

Pasinei chokwadi kuti zviratidzo hosha zvakakwana akaratidza, asi zviri uyewo maitiro mamwe akawanda chiropa zvirwere. kuongororwa zvakarurama uye kuziva zvirwere zvinogona Caroli ari US uye panguva CT. Computed tomography ichaongororwa chimwe chezvinhu anodzidzisa nzira kuongororwa, nekuti unogona kuona zvakanaka zvakakwana ose kutyorwa nemitemo. Uyezve, endoscopic cholangiography kungadiwa kuti chirwere.

Chiropa basa nemiedzo kwenguva refu Zvisinei kuchinja, pamwe kuchiita chirwere uye refu kushoma munyika nokukanganisika kuongorora ropa anogona kuziva zvose nezviratidzo cholestasis.

Nekuti varwere vari pangozi cholangiocarcinoma, kuwedzera yaifanira uye serological kuongorora kuvapo bundu zvezvinangwa.

Features kurapwa

In pamberi Caroli chirwere kurapwa nhungamiro inofanira kuchengetwa haambokundikani, nekuti zvokurwara iri mberi zvakasikwa. Treatment zvinoreva kubudikidza nokushandisa mishonga inorwisa mabhakitiriya, uye ursodeoxycholic iine acid Kutarisirwa mamiriro kudzivirira calculus inotungamirwa.

Mukuwedzera, kurapwa unotora:

  • analgesics;
  • litholysis mabwe;
  • biliary abudise.

Pamusoro accession, cholangitis, kana zvimwe matambudziko anoitika purulent mishonga hapana vakasiyana kurapwa kwemabhakitiriya cholangitis. Zvakakosha kuti kubvisa urwa uye ipapo yokunatswa rinoitwa kubva bile mutsinga dzinofamba nemukaka, uye vakashandisa mishonga kubatsira kubvisa chirwere.

The oparesheni rinoitwa chete panyaya kakawanda exacerbations kana kushandisa basa kuti kuchinja nzira. Bhuku kuvhiya kupindira anogona zvakasiyana-siyana. chete matombo kana biliary ndima inogona kubviswa.

Kana simba kwazvo kuwedzera ndima uye biliary bile kurega kunotanga, chiremba anogona kuitisa kubviswa imwe akafukidza chiropa. In Muzviitiko zvakaipisisa, hepatic insufficiency pamberi kana zviratidzo degeneration ari akaipa bundu, chiropa anogona varumbidzwa kubva yepedyo.

Nokuti migumisiro yakanakisisa, vanachiremba vakawanda dzinorumbidza tikapedza chiropa transplantation kunyange kusavapo kwazvo zviratidzo zviri kutanga nzendo chirwere. Zvisinei, kazhinji, kuvapo chirwere chinhu contraindication kuti transplantation. Varwere wokurarama pashure transplantation pamwe vachiberekwa fibrosis kuti vave anowedzera chirwere cholangitis panguva transplantation, iri nani pasi.

Fungidziro chirwere ichi zvikuru vanoshorwa, sezvo zvazvo kunogona kuitika pamusoro akawanda. Zvisinei, zvikuru kashoma zvinoguma rufu murwere.

Caroli chirwere

Disease Caroli kazhinji chokuita vachiberekwa hepatic fibrosis, zvichiguma ane Caroli chirwere. Vaviri pathologies idzi inoumbwa ne rinenge kufanana chimiro biliary zvinetso zviri chiropa rinenge pachiyero embryo kukura. The chirwere iri nhaka yepedyo uye hwakaratidzwa abdominal marwadzo uye nekudeura ropa kubva esophageal varices. Neonates angava mubatanidzwa huru zviratidzo vachiberekwa hepatic fibrosis, Caroli chirwere uye polycystic cheitsvo.

chirwere ichi zvinoreva vachiberekwa bile mutsinga dzinofamba nemukaka chikofu Zvisinei, kashoma zvikuru uye zvikurukuru vanhu vane makore pasi pemakore 30. Mumakore mashoma makore zvokurwara okutanga kunoitika zvachose asymptomatic, sokuvapo pakuwedzera bile ducts musanetsa kurega kunotanga kubva bile, izvo achasika ezvinhu kuti paumbwe mabwe accession hweHIV. Kana kushandiswa pamwe nevamwe akaona zviratidzo jaundice, inoratidza kuvapo cholangitis.

It vakapemberera kunyanya kuruboshwe madziro kukuvara chiropa, asi rinogonawo kuva maviri-nzira dzimwe nguva.

Mune zvimwe zviitiko, chiropa chakasimba zvokuti rinogona kukanganisa dzimwe nhengo. Saka rimwe yematambudziko anogona kunzi sezvo panowanikwa renal kukundikana.

Similar articles

 

 

 

 

Trending Now

 

 

 

 

Newest

Copyright © 2018 sn.birmiss.com. Theme powered by WordPress.