UtanoZvirwere uye Conditions

Chorea - a ... Chorea muvana. rheumatic chorea

Chorea - mumwe zvokurwara pakati tsinga. Rinoreva siyana hyperkinetic. The chirwere achabatsirwa matambudziko chepfungwa subcortical nodes. Inogona kuziva maitiro zvinhu: ane episodic, vasina chinangwa, runobva twitching ramaoko nemakumbo, dzimwe nguva ari hunde. In akazotevera matanho pane pfungwa nevakangwara nokuremara, nezvinetso kufambisa, uye nokuzvidzora basa. Vana chorea kazhinji kururama kuti kwomuzvarirwo basa kwakawedzera. Kutaura zvazviri, kana zviratidzo chirwere kutanga kutsvaka rubatsiro vakakodzera.

Shoko rokuti "chorea"

Izwi iri rinoshandiswa nyaya mbiri. Zvinogona kureva yakazvimirira chirwere, izvo ndezvaJehovha boka iri (semuenzaniso, duku Huntington chorea kana chorea). Uyewo rinoshandiswa kutsanangura zvimwe syndromes zvinoitika mhando apo zvakasiyana zvirwere. Shoko "chorea" rinobva mutauro wechiGiriki, umo anoratidza kuti kutamba imwe mhando. Izvi inotsanangura Zviratidzo zvokutanga, iyo vanoratidza vari mawere, uncoordinated, jerky, kukurumidza fambisa hunde uye migumo. Unhu murwere zvechokwadi akaita involuntary, runobva kutamba. Noumwe nguva inonzi chorea "St. Vitus dance." Zita iri chokuita yekare dzidziso St. Vitus, iyo achishingaira kupararira chiKristu, yaakanga akatambudzwa nevarwi veRoma. Pashure pokufa kwake akava akakurumbira ngano kuti kana mumwe munhu aite chinoshingaira kutamba akapoteredza guva rake pazuva raakaberekwa achaita kuwana mutariri vivacity uye nesimba rose gore.

zvikonzero

Zvinokonzera chirwere angava akasiyana mavambo, asi zvikurukuru chorea kukonzera nhaka zvinhu kana nemagene zvirwere.

Ishoma chorea, kunokonzerwa kwakadaro zvinotapukira hunhu zvirwere zvakadai TB yomumuzongoza, nemavhairasi encephalitis, neurosyphilis, chirwere cheLyme, whooping chikosoro. Panowanikwa chorea anogona chokuita metabolic vanotaura (kana pane chirwere Fabry kuti, hyperglycemia, hyperthyroidism, kana Wilson nechirwere), intoxications (Kusvibisa nemumuromo nhumbu, mekuri, lithium, digoxin, neuroleptics, levodopa), autoimmune pathologies (akadai antiphospholipid urwere , chinonzi systemic lupus erythematosus, multiple sclerosis). Pakati zvikonzero kuti kutsamwisa panowanikwa chirwere, vanachiremba anonziwo uropi zvivako. Izvi zvinosanganisira bundu inotungamirwa, hypoxic encephalopathy, dzechimwe uropi makuvaro, kurohwa.

Common zviratidzo

Chorea - chirwere hworatidza pacharo asingashumbi, ita mhirizhonga, pfupi pamuviri masangano. Mune zvimwe zviitiko, masangano aya anogona kutorwa sechinhu chakajairika, pokugara, kwese kuti utano munhu, chinhu mwoyo. Vamwe, akafanana mupfungwa, chin'a kutamba. Jerky pfura zvinogona one- kana maviri-madziro, asi havana panguva mudukusa synchronicity zvimwe mhando.

Zvichienderana chii akawanikwa muchimiro zvokurwara, kusiyanisa zviratidzo chorea. Kana munhu zvishoma haana trochaic hyperkinesis, ipapo maitiro ake ari kuchengetwa injini kuduku hanya, achiperekedzwa gwenya disinhibition, vakawedzera emotionality, nevamwe unhu, fidgeting, kukodzera nemasaini.

Vakasiyana siyana pachena sezvo chorea kufamba chairwo "vad-vad". Zvakakomba chimiro trochaic hyperkinesis inokanganisa inofamba kufamba, kutaura uye zvaunoita chiso chako. murwere gait hakusi chete chinoshamisa, asiwo vamwe nechiyero "chigure". Chorea, zviratidzo zvacho zvakaoma, haabvumiri kunyange kuita zvimwe mapato. Varwere nehosha kwazvo pasina zvakavapoteredza, sezvo hazvina kufamba uye anogona caterers woga muupenyu zvakazara.

Huntington chorea

zvokurwara Izvi zvinoratidza pacharo kakawanda pakati pemakore 35 kusvika 45 makore. Chorea, zviratidzo izvo, kunze hwokufananidzira hyperkinetic, takura zvakawanda unhu zvinetso uye dementia (kuderera mune ungwaru) anova zvishoma nezvishoma, dzimwe nguva zvakaoma kuti kuronda nguva apo akatanga kubuda. Yokutanga kufamba chisimba kazhinji kuitika pachiso. Vanogona kuvhiringidzwa kurongwa injini automatisms (yakabudikira rurimi ichi, frowning, licking miromo, muromo yokutanga). Kuchiita maperembudzi richiratidzwa kukura hyperkinetic ari hunde uye migumo. Zvakakomba chimiro dzinoratidzwa impairments hwekutaura, ndangariro, pakuparadza chichiitwa, padanho kuzvikoshesa basa uye rinopera dementia. Tanga nokuti Huntington chorea vari chirwere chepfungwa muchimiro hallucinatory-paranoid, kuvhiringidzika uye maitiro asina kutsarukana.

Neyroakantotsitoz

Varwere Neyroakantotsitozom musatendera chete trochaic hyperkinesis, asi acanthocytosis (kuchinja anoumba masero matsvuku). Runoratidza zvokurwara iri atrophy (kusimba tsandanyama ose okumusoro migumo). Zvimwewo Unhu kusiyanisa zvirwere: nomumukanwa hyperkinesis pamwe kutsenga kufamba, jerking muromo yakabudikira rurimi uye nevamwe zviso. Kana neyroakantotsitoze murwere involuntarily iskusyvaet rurimi rwake, miromo uye namatama womukati pechiso ropa. A complicating chinhu chirwere ichi uye dementia protrude pfari.

Disease Lesch-Nai Han

Vachiberekwa zvirwere tsinga kupindira munhu kurarama upenyu huzere. Izvi pathologies chokuita nezvirwere uye Lesch-Nai Han. Kukonzera chirwere ari nhaka kushayiwa hypoxanthine-guanine. chorea ichi muvana achabatsirwa zvakakomba kuvhiringidzika nokushanda kwenhengo tsinga. Uyewo zvokurwara wakatsamwisa rakawedzera kugadzirwa uric acid.

Kubva mwedzi upenyu chokutanga mwana waona chinhu kunonoka kukura. The Rigidity maoko nemakumbo kunoratidzwa nomwedzi wechitatu. Kubva gore upenyu rechipiri mwana ane chiso grimaces, ayo achiperekedzwa zviratidzo pyramidal turakiti maronda uye kunonoka kukura mupfungwa. Baby anogona kukuvadza utano pachavo nokuda kuruma miromo yavo kana minwe.

benign chorea

Benign Chorea muvana kunooneka pacharo ari pazamu kana muduku. Zvokurwara zvinoreva nhaka zvirwere. Generalized hyperkinesia mune chirwere ichi vanotiza chete kana mwana akarara. Kubva Huntington chorea, kwakadai zvokurwara rakasiyana vasiri progressors uye chakaipa kukura yenjere. In vakwegura zera iri benign chorea Unogona kuderedza hyperkinetic, kana nguva kuonana zvokurapa chivako.

Secondary siyana chorea

Vakawanda yechipiri siyana chirwere vanoonekwa maviri: chorea uye chorea akazvitakura.

Yokutanga inonzi Sydenham kuti chorea. Chitarisiko wake anogona kutsamwisa chakasimba streptococcal noutachiona kana rheumatic fivha. Munyoro chimiro kunoratidzwa kuwedzeredzwa grimace, anotaurisa nhengo dzomuviri, masangano disinhibition. More kunzwisisa siyana trochaic hyperkinesis wakaratidzwa chokwadi kuti murwere zvakaoma kufamba, kutaura zvakanaka, kunyange kufema. Kana chirwere kunoitika se "tonic" mabvi uye hunenge "isingarapiki", mupfungwa uye kuvhiringidzika nepfungwa, tsandanyama neBP.

Pregnant chorea - chirwere akadzokera kubva pauduku. Ndiko, ari pangozi mapazi ndivo vakadzi vanenge vasangana mwana muduku kwaya. Zvokurwara anogona kuitika panguva yokutanga pamuviri nokuda 2-5 mwedzi. In haizopereri nzira "inonakidza" mamiriro ezvinhu Zvingamukawo chorea. Treatment Pakadaro hadziwanzowaniki, sezvo chirwere haazombotaurwi roga pashure ane chidzivaidzo pamuviri kana pashure yokusununguka.

chorea rheumatica

The panowanikwa chirwere chinouya pakati kwakawedzera rheumatic fivha kana endocarditis, icho pamwe valvular mwoyo chirwere. Kakawanda kacho chirwere havasi akarondedzera chinhu ichi, uye chirwere anoratidza pacharo tisingatungamirirwi.

Rheumatic chorea kazhinji inokanganisa vana pakati pemakore 6 15 makore. In vasikana, asi zvokurwara ndiye anonyanya. In wokutanga Danho chirwere chinogona kuva chikonzero chokunetseka, nokuti zviratidzo vari achingopiwa grimaces, uye vabereki uitore wosekwa. Muitiro duku involuntary fambisa maoko nemakumbo, kutanga zvigunwe uye zvishoma nezvishoma kuparadzira yose muviri. Papera vhiki rinouya muenzaniso nguva, apo mwana kufamba vari kutsanya uye kwakakwana. Ichi kunodzivisa mwana kuramba kuipa kushandiswa, ndiko, kuti adye, kufamba, kunyora.

Rheumatic chorea zvinokanganisa hwomwana kumeso zviuru grimaces. Chakakomba siyana hosha kuvhiringidza murwere kuti kumira, kumedza, kutaura, uye muviri yairamba ichifambira. Kana nechirwere chorea, kurapwa yaifanira kwazvo uye nokukurumidza.

Diagnostics

Vanofungidzirwa chorea simuka nokuda chinoshamisa maitiro. Mune rokutanga kuongororwa, chiremba anofanira kuchengeta kukurukura murwere kana mhuri yake. Akanyanya zvakakosha kuziva kana mumwe anorwara zvimwe mumhuri chirwere ichi, refu sei vakanga chorea zviratidzo, kana murwere madhiragi, kana zvirwere anogumbura kutambudzika. Uyezve nyanzvi anofanira kuongorora involuntary kufamba. Zvinokoshawo kuti chirwere uye tsanangudzo zvirwere zvinogona achiperekedzwa chorea, kukonzera zvakakomba rezvedzidzo kutsauka. Zviratidzo zvirwere izvi regai pachena nguva dzose. Dzimwe nguva, kuti rione abnormalities zvakadaro vachiri danho, mumwe kunzwisisa rinoitwa kuongorora. A bvunzo ropa acharatidza padanho mhangura muropa uye kuvapo kana kusavapo zviratidzo anogumbura siyana. Uyezve, basa kombiyuta tomography, rinobva resonance kuri, electroencephalography.

mabatiro

Chorea - a zvokurwara kuti haibvumiri murwere kuitisa zvatinosiita upenyu huzere, saka kunofanira kurapwa nenguva uye izere. Nzira kurapwa kunobva zvirwere zvikonzero. Somuenzaniso, muna Wilson nehosha murwere ushandiswe zvokudya pamwe risingamboshandisi zviri zvemhangura uye zvinodhaka ane zvinoitwa kutaurirwa mukuderedza Absorção de Água wayo.

Chorea Huntington ushandiswe neuroleptics uye benzodiazepine mapiritsi. Kana chorea kukonzerwa chisingaperi insufficiency ropa aibuda chepfungwa pane vanoda mishonga kudzikisa BP. Vasculitis akatakura hormone kurapwa. Kana iwe kuonekwa generalized chaizvo zviratidzo, kurapwa kunofanira dzakaoma.

Kuderedza involuntary fambisa runobvira pachishandiswa kuvhiya kupindira, kana kuparadza ventrolateral musimboti thalamus. Chorea vanofanira kutora zvinodhaka kuti kuvandudza kushanda pfungwa uye zvokudya, uyewo mavhitaminzi kuti boka B.

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