UtanoZvirwere uye Conditions

Fused zvigunwe: Zvinokonzera neMarapirwo

Nei vamwe vacheche vanoberekwa fused nezvigunwe? Ko chinhu abnormality yakadaro, uye anogona I kuchiparadza? Mhinduro dzemibvunzo iyi nemimwe mibvunzo pamusoro zvarakasiya ataurwa zvinhu uchadzidza kubva ino.

General ruzivo pamusoro zvokurwara

Fused zvigunwe - chinhu vachiberekwa yakaderera nemakumbo kukura. kutsauka uku kunoratidzwa kukwana kana kwakakwana Fusion zviviri kana kupfuura mimwe. In okurapa, fused zvigunwe vane zita chairo - syndactyly.

With chirwere ichi muvanhu angava Fusion zvose akaremara uye underdeveloped minwe uye zvakanaka yakatanga. Mhedzisiro syndactyly ndiyo yaishandiswa uye zvizorwa kuremara repasi richiripo.

Mbudzana pamwechete kutsaudzira anofanira kugara akabvunza mumwe geneticist uye Chiremba Wemabhonzo. Kuti asimbise chimiro syndactyly, yaifanira X-ray norutsoka. Treatment kuremadza ichi rinoitwa chete kuvhiyiwa. Panyaya iyi, vaviri fused zvigunwe vanoparadzaniswa uye vaishandisa purasitiki uye kuremara kuvhara kana zvakakodzera chaizvo.

vamwe nhamba

Syndactyly akadana zvemamiriro kukura munwe iri nemhaka kutyora vaparadzane zvakanaka. Kazhinji, izvi zvinoitika panguva embryonic nguva.

Fused nezvigunwe achangoberekwa mwana akawanikwa aine kakawanda 1 kusvika 3000. Zvinofanira kuzivikanwa kuti syndactyly iri hafu vose vachiberekwa anomalies. Kwakadaro rutsoka zvokurwara vangava yakazvimirira Kutsauka, uye pamwe chete nevamwe kuremara (semuenzaniso, minwe hypoplasia, polydactyly uye polifalangiey, ectrodactyly, brachydactyly, brachioradialis synostosis, kukamurwa brushes, ulnar kana TOUR clubhand uye zvichingodaro.).

Inenge 60% yevana maari vari fused zvigunwe (Photo gwapa munyaya ino), zvinobatana vachiberekwa abnormalities ari locomotor ino (semuenzaniso, pseudarthrosis, clubfoot, zvemamiriro vanorega chikwata uye zvichingodaro).

chinokonzera ndiko kuremara

Sei vana vave mutevedzeri zvakadaro, kufanana fused nezvigunwe? The zvinokonzera kutsauka ichi kunogona kuva akasiyana. Nyanzvi dzinodavira kuti muna 20% nyaya izvi rakabva kuvabereki. Nemamwe mashoko, vose mhosva ane autosomal chikuru mufananidzo nhaka.

Kana nhoroondo mhuri syndactyly chinoshayikwa, zvinofanira vakafunga kuti kutyorwa Kusiyanisa uye paumbwe dzapasi mapazi ari mudumbu yakaitika munguva embryogenesis. Kazhinji ichi chinoitika kana paine matambudziko siyana nematambudziko zvinhu.

A urema hwapedyo?

Sei makumbo fused minwe, uye sei kutsanangura rimwe gumbo kukura kwakadaro? mwana ramangwana Anodzivisawo nokuturika paruchaitika chechi5 vhiki intrauterine kukura. Panguva iyi iri mudumbu anogona kuva vasiri syndactyly.

Pasina zvakakanganisika kare muna 7th vhiki minwe vari aumba. Izvi imhaka kuwedzera nomunwe mwaranzi uye kuderedza kukura interdigital zvikamu. Kana rutapudzo ari interdigital masvingo kuputswa, ipapo phalanx haina vakaparadzana, kuti pane syndactyly.

Possible zvikonzero kanganisika budiriro

Fused nezvigunwe, mwana anogona kuitika munguva ine chepfu migumisiro iri muviri womukadzi pamuviri. Kazhinji ichi kunoitika panguva kunwa mushonga, zvinwiwa zvinodhaka, uye muna vanoshorwa ikoroji, inobudisa basa, X-ray irradiation, uye zvirwere (semuenzaniso, yokuSpain, njovhera, tibhii, etc.).

Kazhinji zvinokonzera kuberekwa kwemwana pamwe syndactyly kuramba kujeka.

Fused nezvigunwe - chinowanzoonekwa vakachengeta kuremara mukati sechivako chromosomal uye nemagene syndromes.

Zviya, iri chaizvo kashoma kuwanikwa vanhu vawana syndactyly. Kazhinji, kwakadaro zvokurwara inomuka pashure rutsoka kutsva (thermal kana mushonga).

Fused nezvigunwe - zvinoreva zvokurwara ichi?

Vanhu Vakawanda vanoshingaira anoitiswa chakavanzika, zvinofungidzirwa kuti zvokurwara ichi anovandudza kwete chete. Zvinofungidzirwa kuti ichi mhando mutation ndiyo diabolical. Zvechokwadi, fused minwe rakanyatsojeka nowenyika akaparadzana.

Asi vanachiremba vanoti hapana chinoshamisa uye anotyisa pakuti hapana rutsoka kukura. Izvi inongova anomaly muzvidimbu kubva iri chaizvo nyore kubvisa, kunyanya tanga upenyu hwemwana.

Naizvozvo musafunganya zvikuru kana uri fused zvigunwe. Izvozvo zvinorevei, unogona kutaura chete chiremba, kwete diabolical vadiwa zvisiri.

kupatsanura urema

In orthopedics syndactyly graded maererano kureba, mhando musono, uyewo mamiriro minwe.

Parizvino kusiyaniswa:

  • pfupa chimiro (kana pfupa Spike kunoitika);
  • nyoro zvinyama chimiro (dzimwe nguva membranous uye ganda).

kuremara kupatsanura urefu kunobva nhamba uye urefu phalanges fused musono.

Achitaura mamiriro fused minwe, kuti syndactyly zvinogona dzakaoma uye nyore. Mukupera zvazvingava, Fusion pamusoro kwomuzvarirwo nezvigunwe, uye wokutanga - pamwe abnormalities pfupa, vadyi, mudzira kana shwashwa midziyo.

nemagene marudzi

Syndactyly Classified uye nemagene mhando:

  • The mhando wokutanga - zigodaktiliya. Mienzaniso kana kwakakwana Fusion (membranous) 2nd uye 3rd toe. Uyewo haana aibata vamwe webbed minwe.
  • The mhando rechipiri - sinpolidaktiliya. Fusion of 4th uye 5th nezvigunwe ane doubling pamusoro 5th. Nokuti zvokurwara ichi kunoratidzwa: kutyorwa reliefs nedehwe inotsika uye hypoplasia yapakati phalanx.
  • The mhando wechitatu. Two-nzira kwakakwana syndactyly pamusoro 4th uye 5th minwe. Panyaya iyi, tsoka hauna kukanganiswa.
  • The mhando chechina - syndactyly Strip. Full bilateral cutaneous syndactyly ruoko. Panguva iyoyo hapana vanorega kurasikirwa.
  • The mhando wechishanu. Kubatanidza metatarsal uye mapfupa metacarpal. On maoko zvikuru zvinozivikanwa 3-4 Fusion reminwe netsoka - 2 uye 3 ,.

kuremara zviratidzo

Kana syndactyly wetsoka ari mwana kakawanda vakachengeta Fusion pamusoro 2nd uye 3rd nezvigunwe. Panguva Batanidzai phalanx chinogona underdeveloped kana dzakabudirira kupengereka. Mune zvimwe zviitiko, pane kuderera kwenhamba minwe, nokuda kwavo Líquido kudimurwa.

Kusiyana vana syndactyly mumaoko vana syndactyly tsoka kuva zvikuru kupengereka. Havachina nezvinetso Implementation munhu akasiyana denderedzwa kuita. In ichi dzichipfekeka kushayiwa norutsoka haana kuoma kudzidza, uyewo anenge kumbobvira ichikutadzisa kusarudza basa ramangwana.

How rokuongorora?

How rokuongorora fused zvigunwe (chiratidzo chokuti kuremara kwakadaro rave richirondedzerwa zvishoma papera)? Syndactyly padzakacherechedza neonatologist pakarepo pashure pokuzvarwa mwana. Humwe akataura vomwana rinoitwa chiremba orthopedics kana kuvhiyiwa. Kuti siya chromosomal naGene abnormalities zvinogona kwakabatana uye genetics.

Pasinei chokwadi kuti wakadaro chirwere chinoitwa pashure kutarisana vaongo- kujekesa mhando kuremara, uyewo kugadzirwa kwepurogiramu kurapwa nzira, zvinokosha kuti azodzidza chokushandisa.

Radiography rutsoka mu maberere maviri achibvumira nyanzvi kuti kufungidzira arambe achirema kuti mapfupa, vadyi utano, kureba uye kuvapo mapfupa Fusion. Kuziva unhu ropa kuyerera uye vascular samambure mu minwe kuita UZDG, reovasography, angiography uye yemagetsi lämpömittari.

kurapwa chirwere

Pane mushonga fused nezvigunwe? Operation yokuparadzanisa phalanges - chete Zvingangokubatsirai. Zvisinei, zvinofanira kucherechedzwa kuti kuvhiya rinoshandiswa chete syndactyly pakati minwe. Achitaura fused phalanxes kurega, muchiitiko ichi, kuvhiyiwa hakuratidzwi. Kana abnormality kwakadaro kuzvirega zvichikanganisa dzose kufamba, ari kupindira richiri kuitwa.

Kana kuvhiyiwa kuri kuitika?

Terms uye nzira kuvhiya kupindira takatsunga inobva hunhu uye chimiro ndiko kuremara. Chinangwa kurapwa iri kurambidza kuremara zvizorwa, uyewo kuwedzera mashandiro tsoka kana ruoko.

The optimum nguva oparesheni - makore 4-5. Kana achangoberekwa ari kuchengetwa syndactyly pakupedzisira kupindira rinoitwa yechipiri hafu youpenyu hwake. Kanoita deformation pakati yechipiri minwe uye gogonera ikure phalanges.

zvomusejari Nzira

Panguva mashandiro inotevera zvomusejari nzira vanogona kushandiswa:

  • kupatsanurwa conjoined minwe vane ganda plasty dzomuungano munyama;
  • membranous Kuparadzana musono skinless mapurasitiki;
  • fused kuparadzana minwe, izvo kuzadzikiswa nokushandisa ganda kusonanidzwa naye vakasununguka autografts uye nemakanzuru munyama zvabatanidzwa;
  • kupatsanurwa conjoined minwe, izvo nechimwe wakasununguka ganda kusonanidzwa polnosloynym kana kutsemura ganda batanidza;
  • multi-Danho kupindira pamwe mudzira-tsandanyama, ganda uye skeletal mapurasitiki.

The postoperative kumwedzi

Pashure pokuvhiyiwa, kuvakanganise pabazi vakaparadzana minwe kumanikidza bvisika purasita chitsamhura. Zvinokurudzirwa kupfeka kanenge 3-4 mwedzi.

Inenge mazuva 15 mushure oparesheni vanotanga murwere apore. Kuti aite izvi, shandisa masaja maoko kana makumbo, kurovedza muviri kurapa, phonophoresis pamwe Lydasum, zvemagetsi kweiyi tsandanyama eminwe, ozokerite, Paraffin uye madhaka Achiputira.

Mugumisiro hwokushanda

Nzira inoshandiswa Kuvhiya kurapwa ano syndactyly kupa zvizorwa zvakanaka uye dzichipfekeka zvabuda. With nenguva kupindira kwete chete zvakakwana ichadzorerwa kuipa yakarongeka, asiwo bhurasho kushanda rutsoka.

Surgery kubvisa syndactyly akabudirira kana murwere asina tightening mavanga uye lateral wakarebesa pamusoro minwe, uye pane zvakawanda izere inofamba iri interphalangeal vadyi (adduction, yokururamisa, kuwedzera uye flexing), rwakabata chepfungwa (panyaya mumakwenzi), nehanya zvakanaka uye zvakasikwa chimiro zvikamu pakati minwe.

Kana kurapa syndactyly vakasarudza kuita, zvinogona kuva inokanganisa kukura uye kukura kwemwana maoko nemakumbo.

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