Utano, Zvirwere uye Conditions
Vasculitis vomwana: Hemorrhagic, sema. Zvinokonzera, zviratidzo, nemifananidzo, kurapwa, fungidziro
Vasculitis akatumidza boka rose pathological ezvinhu. Vanobatana nomumwe nevakawanda chikabviswa - kuzvimba pamadziro midziyo ropa, zvichitungamirira kukuvara kwavo uye kuparadzwa zvishoma nezvishoma. Raigona pangozi huru mutsinga uye arteries uye capillaries diki. Mberi chirwere kukanganisa dzakapoteredza zvinyama uye nhengo dzomukati, izvo kuchambokanganisa wavo wenguva inoshanda uye zvinovhiringidza muviri wose.
Zvokurwara kunokanganisa varume navakadzi vemazera ose. Zvikurukuru ngozi zviitiko apo pane vasculitis mwana. Young saibva muviri havagoni kukurira chirwere. Panguva Chaiyo kurapwa kuti rubatsiro kudzivisa matambudziko.
Mhando dzakasiyana-siyana vasculitis
Vasculitis pamwe chete na anoverengeka nzira: rudzi uye mwero kukuvara midziyo ropa (arteries, mutsinga, capillaries), pfungwa nzvimbo, ayo saizi, etc. Izvi zvinoita panzvimbo kuoma patsanura navo, mukuwedzera, chinowanzoonekwa yakadzokororwa .. Zvisinei, tinofanira kupatsanura pakati mapoka maviri vasculitis:
- maitiro - kunokonzera kukuvara nyama uye nhengo, nokuda kutyorwa ropa ravo zvitengeswa;
- ganda - kwakaratidzwa muchimiro wakananga ganda mapundu, kashoma kutungamirira matambudziko.
Uyewo pane chikuru chinokonzera panowanikwa vasculitis vari akakamurwa inotevera mapoka:
- chikuru - yakabuda sezvo vaakasarudza chirwere nokuda mumwe kukundikana masoja zvigadziriswe;
- yechipiri - kuzomukazve pamusoro zvimwe zvirwere (chirwere, nemavhairasi, parasitic, etc.).
Vasculitis vomwana uye mukuru ari pachena kuti mumwe chete kupatsanura.
vasculitis sei ngozi vana?
Kana vasculitis ikabuda mwana, hazvina kunowedzera ngozi pane generalized aibuda, t. E. rakapararira muviri. Unformed muviri mwana haagoni pachawo kutsungirira chirwere rikurumidze, uye chirwere mberi nokukurumidza. Saka, zvinogona kungoitika kuitika mune rikwanise chimiro. Uye pashure kupora kazhinji kudzokazve.
Fever, mukuru kudzikira, kurasikirwa kudya, tsika mapundu anokonzera kusagadzikana uye kuvaviwa - zviratidzo iyo munhu anogona kuziva vasculitis Vana (predsavleno mufananidzo pazasi).
Kana paine matambudziko anoitika vasculitis anogona dzinoyerera kupinda vamwe zvikuru kwazvo siyana. Ipapo vakashamiswa midziyo kwete ganda, asiwo makuru uye zviduku arteries, mutsinga uye dzimwe nzvimbo dzomuviri uye nhengo dzomukati. Tsandanyama uye mapfundo havawani zvakakwana zvinovaka muviri uye ropa rakawanda, zvishoma nezvishoma atrophy uye kurasikirwa mufambo. ngozi kwakadaro kunosanganisira vasculitis vana. Treatment uye rubatsiro anokwanisa kunge yakakodzera.
Hemorrhagic vasculitis muvana
Hemorrhagic vasculitis inonziwo chirwere-Hanoki purpura. Enough yakajairika chirwere muvana kubvira 4 kusvika 7 makore asi kunogona kuitika munguva vacheche. Zvinokonzera - kutapurirana zvirwere (nemavhairasi, kwemabhakitiriya), parasitic infestations, akawanda majekiseni, zvokudya nezvimwe zvinhu.
Uchapupu rokutanga zviratidzo chirwere - Hemorrhagic mapundu kunosiyana inosiyana pakudzama. Kakawanda zviri vemunyika pamusoro rezasi migumo, pedo majoini, anokotama. Very kashoma, rashes aonekwa dzimwe nhengo dzomuviri - maoko, tsoka, mutsipa, chiso. Panguva iyi lesion rinopararira mumidziyo diki ganda. Ndiro chiratidzo chikuru zvakatemwa pedyo Hemorrhagic vasculitis muvana.
Zviratidzo manyorerwo chirwere, munogona zvakafanana ane ganda mapundu kana gare gare ayo mazwi. kukundwa uku mapfundo, richiratidzwa sezvo marwadzo, kuzvimba, edema. Possible kubatanidzwa mune pathological muitiro womunhu zvomudumbu ino, izvo pamwe kufundumwara mudumbu, colic, kuda kurutsa, kurutsa.
Pagungano 1 ST kana 2 nd it gore agone kuva mheni chimiro, izvo zvinoomesa zvikuru Hemorrhagic vasculitis vana. The zvinokonzera - kuchinjwa vanonzi vana zvirwere -. Scarlet fivha, huku pox, rubella, etc. The mukurwara ichi nguva dzose chakasimba, chemafuta akawandisa kuratidzwa zviratidzo, uye anogona kuva nengozi vana unformed muviri.
zvekuchipatara siyana
Zvivanakire, mune kurapwa tsika, munhu Hemorrhagic vasculitis inogona dziya munzvimbo inotevera muchimiro:
- A nyore chimiro. Sevatsigiri cutaneous purpura. Kwakaratidzwa muchimiro rwepepuru mapundu - ichi ndicho chikuru chirwere chiratidzo uye chiratidzo. Anowanzodanwa inokanganisa maoko nemakumbo maduku, kazhinji hunopfuura.
- Skin-articular purpura. More chakakomba zvinoratidza chirwere. Kuwedzera ganda rashes, vadyi kukuvara kunoitika. Zvinonzi pamwe nemarwadzo uye kuzvimba. Zvikurukuru kukanganiswa ibvi majoini, dzinenge - kugokora uye chiningoningo.
- Abdominal purpura (urwere). Achiperekedzwa marwadzo uye unopinza kurwadziwa mudumbu, kurutsa, kuda kurutsa. Kana chete vane chiratidzo ichi Zvakaoma chaizvo rokuongorora mumwe Hemorrhagic vasculitis muvana. Zvinokonzera hosha - kukundwa of abdominal zvomukati, dzinova nemudumbu.
- Nephritic syndrome. Kazhinji anovandudza pamusoro pakanyorwa dzimwe zviratidzo chirwere.
- Mixed chimiro. Inogona sangana vaviri kana zvose 3 zviratidzo.
- Rare siyana. Runoratidzwa zvemapapu chirwere, tsinga uye nhengo dzokubereka nadzo. Kuitika mune zvisingawanzoitiki zviitiko.
zvinokonzera
Hemorrhagic vasculitis ndezvaMwari zvirwere kunzwisisa chirwere. Parinowanika uye kufambira mberi masoja zvivako havagovani - muropa achiparadzira antigen-antibody remubatanidzwa (AH - AT).
Kazhinji zvivako AT - AG aparadza chaiyo ropa masero - phagocytes. Asi dzimwe nguva vanogona kuunganidza mu muropa, "agadzirise" iri pedyo, chikonzero kuzvimba munyama uye zvomukati. Kunze chiitiko AG - AT zvivako anowedzera permeability ari mudziyo pamadziro, zviri activation of mukwanisi hurongwa - mapuroteni zvinobatanidzwa masoja mhinduro. Maererano parameters izvi, rabhoritari chirwere chiri kuitwa.
chirwere chirwere
Vasculitis of mwana akanzi nevanhu anotevera zvimwe:
- Kuvapo ganda rashes nezvishava uye nezvitsvuku hues. The mavara ose dhayamita duku, convex chimiro. Anogona musiwa chero chikamu muviri, asi kakawanda - panzvimbo dzapasi migumo.
- Abdominal (kubva muchiLatin dumbu -. The mudumbu) marwadzo. Pangava inoratidza, awedzera pashure ose kudya.
- Biopsy (tsvakurudzo chomudziyo rinenge) masvingo venules kana arterioles chinoratidza kuwedzera granulocytes.
Laboratory Data havasi diagnostically chinokosha panyaya iyi. Zvisinei, kuteerera kuwedzera mhando A immunoglobulins muropa serum. Uyewo zviratidzi zvinokosha zvinogona mukuru titer antistreptolisin-O (ASL-O) uye erythrocyte sedimentation mwero (ESR), icho chirwere vasculitis vana.
Zvaifungidzirwa Zvingava zvakanaka hunhu. Mune zvimwe zviitiko, zviratidzo inonyangarika pashure anenge 30 Mazuva mushure chakasimba zvinoratidza chirwere. Zvisinei, pane ngozi renal kukundikana, nemamwe matambudziko ari nemudumbu kana epfungwa.
Hemorrhagic vasculitis muvana: mabatiro
Mabatirwo Hemorrhagic vasculitis kutanga chete pashure kwokupedzisira kugadzwa nyanzvi chirwere uye zvinokonzera chirwere. Treatment achaenderana chokutambudzika chirwere uye mwero kwayo kukura.
Chero zvazvingava kutirambidza locomotor basa. Izvi zvinonyanya kukosha paaiita kusachengeteka kukuru chirwere. Bed zororo raitongwa kusvikira kugadzikana kunyangarika ganda nekumhanyirira. Its avhareji nguva vhiki vanenge 3-4. Kutyora ichi kunogona kukonzera idzokororo Hemorrhagic nekumhanyirira. In zvinoitirwawo chakasimba yematambudziko uye kosi pamubhedha chirwere zororo Kurebesa.
Iva nechokwadi kugadza kudya ine wakaoma anosiiwa zvokudya allergenic uye dzinogona allergenic zvokudya. Kana hosha iri muchimiro abdominal urwere, kuti ndishandise Zvokudya №1. Kuomesa zvinhu zvikuru nephritis - Kudya №7 (siya munyu, nyama, chizi). Kudya kwakadaro kuchaderedza zvinoitika zviratidzo, izvo chinoita Hemorrhagic vasculitis vana.
Treatment, pasinei chirwere, unotora kugamuchira antiplatelet zvinodhaka - zvinodhaka kuti kuderedza thrombosis uye fibrinolysis activators - zvinhu munyaya "Kuparadzwa" clots ropa. Murwiyo uye uwandu mishonga, dose kwavo uye nguva kugamuchirwa anoti chiremba.
Sezvo panowanikwa chirwere chokuita kushanda masoja zvenhengo kurapwa kuri kubvisa pamuviri zvivako AG - AT. At chirwere chakakomba uye hakuna contraindications kuitisa zvokuimba rokuchenesa ropa - plasmapheresis. Izvi nzira achabvisa ropa kwete chete masoja zvivako, asiwo pathogenic utachiona, nemaziso notumwe, muchetura.
Sema vasculitis muvana
Chikonzero chirwere ichi - sema kuita. Kazhinji, izvi masoja kupindura mishonga, zvokudya, kana ane chirwere mumuviri. Izvi zvinoguma kuzvimba uye kukuvara nemidziyo ropa, kunyanya paganda. Kakawanda richiwanika muvana kusvikira makore 15 pashure achirwadziwa communicable chirwere kana nzira yokurapwa. Dzimwe nguva chikonzero kuti pane hypersensitivity vasculitis nevana, varege kuva akajeka. Unofanira kuchipatara nhoroondo kwazvo.
The chikuru chiratidzo chiri rakakura mapundu, itchy. It ane chitarisiko mavara uye / kana convex tubercles yepepuru kana yakatsvukuruka-dzepepuru ruvara pamusoro nzvimbo huru ganda. Vakanga kunyanya aonekwa makumbo, dzakatendereka, magaro. Zvichida blistering uye ulceration, scarring kuti wakaremara midziyo. Kazhinji sema vasculitis inotsidza mumwoyo pamusoro yayo mukati shomanana. Zvisinei, zvinogona matambudziko akadai kukuvara zvomukati nokuda zvaipesana ropa ravo rive.
Mhando uye nezvimiro
Zvichienderana dhayamita ari zvakanangwa mudziyo, anokudzwa:
- pamusoro (dermal) sema vasculitis - kunokanganisa capillaries, arterioles uye venules paganda akashandurwa;
- yakadzika kana dermo-hypodermal - apo pathological muitiro kwaibatanidza arteries uye mutsinga kuti unosvikirwa saizi.
Zvichienderana padariro kukura ganda mapundu, pane zvakawanda siyana chirwere:
- papular - rashes bulging, palpable, pigmented;
- vezikuleznaya - akaumba matema (vesicles) mura mukati;
- pustulnaya - kuonekwa in vakazara pus;
- urikanwi - on-panzvimbo pustules kuonekwa necrotic maronda;
- vanga - iri pamwe scarring kuti akakanganisa ganda.
Mabatirwo sema vasculitis
Zvinonzi zvainanga achidzikisa kuzvimba nokuda mishonga. The kurapa vasanganiswa kunosanganisirawo kugamuchirwa zvinoreva achidzikisa pakugwamba (antiplatelet zvinodhaka), kuwedzera vascular matauriro, uye antihistamines kuderedza neutachiona. Kana maperembudzi idzokororo zvakasikwa, haukwanise kutora mishonga inoshandiswa mangwanani, zvinokwanisika kuti muviri yava yakatanga kuramba kwavari.
Kubvisa simba zvokudya sema yomuchipatara vakanzi kugamuchira enterosorbents. zvinodhaka izvi vasunge uye kubvisa tsvina kubva muura, zvomutadzisa navo kupinda muropa. Uyezve, yakaoma kudya kunze mishonga zvokudya anogona unoitirwa zvirwere mhinduro. ndichisunga chiito ichi kana nechirwere vasculitis vana.
Zvinokonzera chirwere chinogona zvakasiyana. Dzimwe nguva, kana zvava kudikanwa, kwoUmambo mishonga anogona kukonzera munhu sema kuita. Ya yokurapa kunoenderana yezvakaita chirwere (Wavy kana idzokororo).
Chii chakakosha kuziva vabereki?
Vabereki vanofanira kungwarira chaizvo pamusoro chero rashes paganda mwana. Kunyange avo kuti sezvisingakoshi pakutanga kuaona. Vabereki zvinokosha kunzwisisa kuti mwana wacho vasculitis zvingaitika mune nemafungu; nguva kukangamwiro chakatsiva zvazvo. Uyezve, zviratidzo kuzodzosera zvichiitika chirwere zvingasiyana avo vakanga kare. Panguva Chaiyo kurapwa rubatsiro rwokurapa kudzivisa nemigumisiro.
Hazvina zvakafanira kuti mwana kubatwa pasina kana akanga vanofungidzirwa vasculitis. In vana, zvingaratidza kuva zvakawanda. Chirwere uye kurapwa kunofanira kuita anokwanisa mukoti. Kunyanya haaratidzi rusununguko wokusarudza immunostimulatory uye zvinodhaka immunomodulatory. Pashure pezvose, chinoita kuti kuonekwa chero vasculitis - kutyora runodzivirira mashandiro muviri wacho zvigadziriswe.
Kudzivisa kuzodzosera kwaita chirwere mwana kunobatsira kuchengetwa nyore matanho:
- Kuderedza uwandu kunetseka zvinoita;
- nechokwadi muviri, kushingaira mararamiro;
- kuvapo chiedza chaiko nesimba;
- vachisimbisa rokuzvidzivirira.
Zvakakosha kunzwisisa kuti chirwere kutakura-mberi mwana pazera duku kunogona anokanganisa ake kukura mumuviri uye mupfungwa.
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