UtanoZvirwere uye Conditions

ALS (chirwere): Zviratidzo uye kuongorora chirwere nzira

The huta kwevanhu hurongwa huri pangozi chaizvo. Ndokusaka pane zvakawanda zvirwere zvakasiyana zvinogona kukanganisa ichi kunyanya chikamu muviri. Munyaya ino ndinoda kutaura pamusoro pezviri ALS (chirwere). Zviratidzo, zvinokonzera chirwere, uyewo nzira nechirwere uye inobvira kurapwa.

Chii?

Pakutanga, unofanira kunzwisisa dzinokosha idzi. Zvinokoshawo chaizvo kunzwisisa kuti Bhanabhasi (chirwere), zviratidzo chirwere ichakurukurwa gare gare. Tsanangudzo abbreviations: atrophic lateral kuoma dzimwe nhengo dzomuviri. Apo chirwere chinobata tsinga dzose munhu, kureva kutambura motokari Tutsinga tunofambisa mashoko utwu. Ivo riri cerebral cortex uye Anterior nyanga musana. Uyewo zviripo ataura kuti chirwere chacho chisingaperi uye zvinosuwisa, panguva harirapiki.

mhando

Kunewo mamwe marudzi vatatu chirwere akadai ALS:

  1. Nguva dziri kure chaiwo. Haina nhaka. Kuti nezvokuvandudzika anenge 95% vose nyaya zvirwere.
  2. Nhaka (kana mhuri). Sezvo wava pachena, zviri nhaka. Zvisinei, nokuti ichi Chirwere kunoratidzwa zvapedzisira kuratidzwa zviratidzo.
  3. Guam-mhando kana Maumbirwe Mariana. Its yakasiyana chinhu kunoratidzwa pamberi maviri pamusoro. Slow Kugadzirwa chirwere.

Zviratidzo zvokutanga

Kuchitaura kuti zviratidzo chirwere wokutanga zvinogona kurapwa uye mune zvimwe zvirwere. Izvi ndizvo chaizvo dambudziko nokunyengera; rokuongorora pakarepo kwakaoma zvisingaiti. Saka, zviratidzo ALS rokutanga ndeinotevera:

  1. Kupera simba. Kumboda totaura muzvitsitsinho uye netsoka.
  2. Atrophy maoko, neutera tsandanyama. Rinogonawo kuitika dysmotility.
  3. Varwere mukutanga nzendo chirwere anogona droop chemabhazi zvishoma.
  4. Dzinoratidzwa nenguva dzirikure kwetsandanyama. Anogona pfura pamapfudzi ake, maoko, rurimi.
  5. Mbabvu simba. A murefu zvinogona kufamba madaro marefu.
  6. Uyewo maitiro chitarisiko dysarthria, i.e. kutaura nyonganyonga.
  7. wokutanga chinetso kumedza vo kuitika.

Kana murwere ane ALS (a chirwere), zviratidzo kukura chirwere pachava, kukura. Next, murwere anogona neapo kunzwa mafaro chisingapembedzwi kana kusuruvara. Atrophy anogona kuitika mutauro uye disequilibrium. Zvose izvi nokuti munhu ari kutambura basa yakakwirira mupfungwa. Mune zvimwe zviitiko, asati pane zviratidzo zvikuru zvinogona kuvhiringa zvishande ushande. kureva dementia anooneka (ichi kunoitika Kazhinji anenge 1-2% nyaya).

chirwere kunoita

Chiizve chinokosha kuti kuziva vanhu vari vanofarira ALS (chirwere)? Zviratidzo kuti kuitika murwere sezvo chirwere chingataurwa pamusoro chii chaizvo ake Chirwere:

  1. nhengo ALS. Wokutanga gumbo anotora nzvimbo kukundwa. Uyezve mberi kutyora richiripo chaitika.
  2. Bulbar ALS. Panyaya iyi, chikuru zviratidzo zviri kukanganisa kutaura basa, uyewo nezvinetso kumedza. Kuchitaura kuti ichi Chirwere mashoma zvikuru pane wokutanga.

nokuwedzera Zviratidzo

Chii chinofanira kuziva murwere ane chirwere akafanana ALS? Zviratidzo zvishoma nezvishoma kuwedzera, muzvidimbu functionality uchaderedzwa.

  1. Zvishoma nezvishoma pane pathological Babinski, kana kukanganiswa vari repamusoro motokari Tutsinga tunofambisa mashoko utwu.
  2. Tsandanyama matauriro, hunenge huchawedzerwa kuti upgraded.
  3. Zvishoma nezvishoma vachashamiswa uye kuderedza motokari Tutsinga tunofambisa mashoko utwu. Panyaya iyi, murwere Uchanzwa involuntary jerking maoko nemakumbo.
  4. In ichi akanaka kazhinji Varwere dzevanhu kuumba mwoyo, pane kuora mwoyo. All nokuti munhu anorasikirwa kukwanisa kurarama pasina rubatsiro, izvozvo atadza kutama.
  5. ALS Zviratidzo uyewo anoenderana ari kufema hurongwa: murwere atanga kufema zvinovhiringidza.
  6. Uyewo, hazvibviri kuti kuzvipira Eenhede. The murwere kazhinji akaisa chubhu kuburikidza munhu uye anogamuchira ose anodiwa kuti kuvapo chikafu.

Kuchitaura kuti ALS vakanaka zvingaitika nokukurumidza. Zviratidzo pane muduku haangavi akasiyana murwere zviratidzo, vane zviratidzo zvokutanga akazviratidza zvikuru paya. Zvose zvinoenderana muviri, uyewo pamusoro Chirwere. With kukura chirwere zvishoma nezvishoma waipedza munhu anorasikirwa tichikwanisa kuzvimirira vapenyu. Nokufamba kwenguva, zvachose vachiramba richiripo.

The mukunopera

Mumazuva okupedzisira nzendo chirwere murwere kazhinji havachanyatsogoni kufema basa, zvinobvira kukundikana kufema netsandanyama. Muzviitiko zvakadaro, varwere vanoda kufefetedza. Nokufamba kwenguva, angatanga abudise kushanda kwemuviri, iyo kazhinji kunotungamirira kuti anobatana chirwere chesekondari, mamwe inouraya murwere.

Diagnostics

Zvatakurukura chirwere akafanana ALS, zviratidzo, chirwere - ndizvo zvandinoda kuudza zvakare. Kuchitaura kuti hosha akawanikwa kazhinji inofanira kubviswa nemamwe matambudziko nomuviri. Kana murwere anotevera chirwere zvinoreva vangaendeswa:

  1. Blood bvunzo.
  2. Tsandanyama biopsy.
  3. X-ray.
  4. Miedzo kuona tsandanyama basa.
  5. CT, MRI.

Kusiyanisa

Kuchitaura kuti hosha ane zviratidzo kuitika uye zvimwe zvirwere. naizvozvo zvakafanira kusiyanisa ALS pamwe matambudziko anotevera:

  1. Remuromo myelopathy.
  2. Kudhaka kubudikidza mekuri, kutungamirira, manganese.
  3. Syndrome mapere bhaa.
  4. Malabsorption syndrome.
  5. Endocrinopathy and said.

mabatiro

Ikakuruma vaiona chirwere akafanana ALS, zviratidzo, kurapwa - ndizvo vanofanirawo kubhadhara vainyatsotarisirwa. Sezvambotaurwa pamusoro, hazvigoni kupera zvachose. Zvisinei, pane mishonga kubatsira kuderedza kosi yacho chirwere. Muchiitiko chino, kazhinji varwere kutora mishonga yakadai se "Riluzole", "Rilutek" (ose zuva kaviri pazuva). Zviri kudzivisa kunayisa pamusoro zvishoma glutamine, imwe pfuma kuti chinobata motokari Tutsinga tunofambisa mashoko utwu. Zvisinei, zviri zvakare kubatsira vari nzira dzakasiyana-siyana kurapa, ane chinangwa chikuru - pakurwisana huru zviratidzo:

  1. Kana murwere Jorodani, iye antidepressants, mapiritsi kungadiwa.
  2. Kana tsandanyama spasm kunokosha kutora tsandanyama relaxants.
  3. Kana waida, yokutindivadza unogona kupiwa, panguva mushakabvu pavaipfuura chirwere - opiates.
  4. Kana murwere anetseka hope, vanoda benzodiazepine zvinodhaka.
  5. Kana paine kwemabhakitiriya kuomesa vanoda mishonga yaunodya (pamwe bass kazhinji simuka bronchopulmonary zvirwere).

Aids:

  1. Speech mushonga.
  2. Slyunootosos kana kugamuchira mumwe mushonga akadai "Amitriptyline".
  3. Tube kudyisa, zvokudya.
  4. Kushandiswa siyana namano anogona kupa murwere kufamba: mibhedha, macheya, achifamba tumiti, anokosha uketani.
  5. Vangada zvokuimba kufefetedza.

Traditional mushonga, jekiseni nokuti chirwere ichi vari maturo. Zvinofanira akati kuti kwete chete nemurwere asiwo mhuri yake kakawanda kubatsirwa chiremba.

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