UtanoZvirwere uye Conditions

Myasthenia Gravis: zviratidzo, nechirwere, kurapwa

Nhasi, kune vazhinji autoimmune zvirwere. Mumwe anogona kubvisa achibatsirwa zvakanaka akasarudzwa kurapa, ukuwo vamwe havana kupindura kurapwa, uye chinhu choga anokwanisa mishonga - kudzivirira exacerbations.

Nyaya ino nezvazvo zvirwere zvakadai myasthenia gravis: zviratidzo, chirwere uye kurapwa zvirwere - zvose nguva izvi achaedza kukurukura zvizere sezvataigona. Uyezve, tione kuti ndiani zvikuru kubatwa nezvirwere, pane nzira kudzivisa dambudziko kwakadaro ikoko.

Chii myasthenia gravis?

Myasthenia gravis chinhu autoimmune chirwere chinokonzera mberi tsandanyama simba. Izvi kunoitika somugumisiro Kukundikana neuromuscular hutachiwana. Kazhinji, nedambudziko tsandanyama kwameso, matadza uye chiso, kanenge - vachiita kufema ushande.

Sezvo nhamba inoratidza, myasthenia gravis kazhinji chinobata vakadzi pakati pemakore, kunyange mumakore achangopfuura vakatanga kunyorwa pakati pevechiduku.

kupatsanura zvirwere

Zvinenge chirwere ose zvinogona Classified ne mhando. Ndaiva asingasiyi, uye myasthenia gravis. Chimiro chirwere kungaenderana siyana zvikonzero pamusoro, saka, tikatarisa yakajairika marudzi.

Zvichienderana nezera boka murwere myasthenia gravis anogona kuva:

  • vachiberekwa;
  • vachangoberekwa;
  • youth;
  • vakuru;
  • Papera Version.

Zvichienderana zvekuchipatara zviratidzo chirwere vari marudzi anotevera anonzi myasthenia gravis:

  • ziso chimiro;
  • zvetsandanyama nemapfupa;
  • pharyngeal-nechiso;
  • generalized.

Zviratidzo mumwe nomumwe mhando chirwere inokurukurwa pazasi.

Zvinokonzera chirwere

Chinokonzera chirwere yasara unexplored. Zvinonzi chete anozivikanwa kuti hosha kunoitika nokuda blockage of zvirwere receptors mune tsandanyama. Somugumisiro, havana kukwanisa kupindura zvichiguma Neural anonongedzera.

The chirwere myasthenia gravis inogona vachiberekwa kana vawana. Chokutanga muchimiro vashoma zvikuru, uye ayo zvikonzero zviri nemagene kunotouraya.

Vawana myasthenia gravis kungazviratidza pamusoro nechekumashure thymomegaly (prostatic hyperplasia isiri yekenza, thymus) kana anomera. Zvishoma kacho, mhaka chirwere aigona kuva autoimmune chirwere, zvakadai scleroderma kana dermatomyositis.

Pane zvakawanda zviitiko apo myasthenia gravis yakatanga tikafunga kenza. Zvikurukuru, nezvezvitadzo bundu sikarudzi (prostate, ovary), zvinenge - chiropa, bapu, uye zvichingodaro.

zviratidzo

Chii zviratidzo chichabatsira kuti chirwere, "myasthenia gravis"? Zviratidzo zvingava zvakasiyana kana kubatanidzwa zvichienderana chimiro uye pavaipfuura chirwere.

Ocular myasthenia gravis chinobata:

  • tenderera tsandanyama ziso;
  • Ziso tsandanyama ;
  • tsandanyama, riri basa nokusimudza yokumusoro fungiro.

Somugumisiro, zviratidzo chimiro ichi chirwere angava sezvinotevera:

  • dzikatadza kungotarira meso;
  • strabismus;
  • chiono miviri;
  • kusakwanisika kwenguva refu nguva kutarisa zvinhu kure kana zvakare anofungidzirwa;
  • vachirembedza rokumusoro fungiro (ptosis).

Wokupedzisira vaiona zviratidzo kungazviratidza chete manheru uye mangwanani zvakakwana vasipo.

Front chimiro myasthenia gravis achiperekedzwa zviratidzo:

  • Kuchinja inzwi, iyo inova "mhuno" uye mapofu;
  • kuomerwa nokutaura (murwere anoneta kunyange pashure kwemaminitsi mashomanana kukurukura);
  • matambudziko nezvokudya yaunodya (murwere kwakaoma chaizvo kutsenga zvokudya zvikukutu nokuda kwekuneta ari runoenzanirana tsandanyama).

Kukurirwa pamusoro pharynx pane mukuru ndingangokuvara mvura ingress kupinda kufema turakiti. Izvi imhaka yokuti murwere haakwanisi kutora zvokudya zvikukutu uye zvinogona kuvhunga, izvo zvinoitika kazhinji. Somugumisiro, zviri hwakazara kukura chido nemabayo.

Zvetsandanyama nemapfupa chimiro maperembudzi pamwe kuneta imwe chikamu muviri. Kazhinji, izvi zvinoshanda maoko nemakumbo. Pane zviitiko apo murwere anogona kunyange kutora zvatinosiita mukombe wemvura kana kukwira masitepisi.

Chinonyanya ngozi iri generalized chimiro chirwere. Kunoratidza neutera ari kufema tsandanyama, izvo zvingaita kuti rikwanise hypoxia uye rufu.

Sezvaunogona kuona, myasthenia gravis, zviratidzo zvacho chaizvo siyana, ndizvo chaizvo uye upenyu-vachityisidzira zvirwere. Ndokusaka zvinokosha kucherechedza chidzoke dambudziko uye kutora matanho ose anodiwa.

Saka, zvinhu zvinotevera kuti ichakurukurwa yechinangwa waiti "Myasthenia Gravis", - chirwere uye kurapwa zvirwere.

SERVICING iri

Myasthenia Gravis - iri chaizvo isingawanzowanikwi chirwere. Naizvozvo, kuti wetsinga havangagoni kukurumidza kuita zvakarurama kuongorora chirwere.

Chii chinofanira kuitwa kuziva mishonga zvinetso zvakadai myasthenia gravis? Chirwere zvingasanganisira:

  • imwe ongororo yakaitwa murwere kuvapo zvichemo;
  • zvekuchipatara ongororo;
  • prozerinovoy kuitisa miedzo;
  • The bvunzo pamwe edrophonium;
  • electromyographic kudzidza;
  • Pakusarudza pachiyero antibodies kuti acetylcholine receptors ari serum;
  • ziso bvunzo;
  • computed tomography pechipfuva;
  • MRI;
  • tarisa zvemapapu basa.

Munguva yokudzidza, zvakakosha kubvisa zvinobvira zvirwere zvose, zviratidzo izvo kusvika pamwero kwakafanana zviratidzo myasthenia gravis. Somuenzaniso, kungava bulbar urwere, anogumbura zvirwere (yomumuzongoza, encephalitis), bundu inotungamirwa muuropi hunde (hemangioblastoma, glioma), neuro-tsandanyama chirwere (myopathy, Guillain urwere, ALS, etc.), cerebrovascular chirwere (ischemic instult ) uye zvichingodaro.

Drug Mabatirwo myasthenia gravis

Zvichienderana zviratidzo, uye pavaipfuura chirwere anogona siyana uye aida mhando yokurapa.

Wokutanga chidobi zvinoda mishonga kuti kuvandudza zvechivhurumukira hutachiwana panguva neuromuscular junctions. Most inowanzoshandiswa nokuda chinangwa ichi zvakadai pharmacological yomuchipatara se "oksazil", "Neostigmine" "Pyridostigmine" uye zvichingodaro. vose vane zvakafanana mhando chiito uye awedzere wevasungwa kuti acetylcholine. mishonga Ava zvikuru abudirire ndichipfeka kubvisa hosha iri tanga ayo kukura, uyewo panguva kutanga nematambudziko.

Chinotevera chinhu chaunofanira kuita - kodzero kuchinja mvura uye electrolyte mwero mumuviri. Izvi zvinoda yakakwana yaunodya ane B mavhitaminzi uye potassium kuitira zvakajairika muviri.

Kuchiita maperembudzi hunosanganisira kuitwa zvoutsinye kurapwa matanho. Zvinosanganisira mu negashiro immunosuppressive mahormone. Pasinei chokwadi kuti zvinodhaka izvi zviri havaratidzi akashivirira nomuviri, kubatsira kwavo kushandiswa chikuru zvikuru zvinogona nemishonga, kunyanya kana Panyaya kwete chete utano, asi upenyu.

Teererai!

Pane zvimwe zvinodhaka kuti vari zvaisambobvumirwa kuti chirwere "myasthenia gravis". Izvi zvinosanganisira Beta-blockers, magnesium munyu, karusiyamu mhandu, nemishonga, aminoglycosides, thyroid mahormone, mapiritsi, morphine, Quinine nomukaka, antipsychotics, barbiturates, uye hypnotics akawanda uye sedatives.

Uyezve, hatifaniri kukanganwa kuti chero mishonga zvinodhaka anogona kutorwa chete pashure chiremba agadzwa, kufungisisa zvose nomumwe zvechadenga muviri.

Kurapa pamwe Kuvhiya

Drug kurapa hakuiti nguva dzose hunokwanisa mugumisiro, uye kubvisa dambudziko. Naizvozvo, kazhinji achifanira kuvhiya kupindira. It, akavapindurawo, zvingasanganisira vakabata mumwe kana maitirwo ezvinhu akawanda:

  • zvokuimba kufefetedza pakuparwa hazvibviri vaingoerekana kufema;
  • plasmapheresis ropa purifier pamusoro kanganisika antibodies, sezvamakaropafadzwa muitiro yaifanira nguva dzimwe nguva;
  • Occupational kurapa uye physiotherapy - kurapa izvi zviviri regai kubvisa chirwere, asi unogona kubatsira murwere kutsungirira nokufamba mukati tsandanyama simba.

Uyezve, zvingava zvakakodzera kubvisa mashoko thymus shwanu kuburikidza kuvhiyiwa.

Chokumisa Sero kurapa

mhando iyi ndichiva kubvisa dambudziko hakusati akawana yakafara mukurumbira, asi zvakadaro zvinokosha kuyeuka uye nezvake.

Treatment pamwe hunde masero zvinobva adipose zvinyama, akaratidza yakakwirira kunyatsoshanda pakurwisa zvirwere zvakakwana. Dzinoita kuti pave kunonyanyisa kuwedzera nguva kanganwiro. Healthy hunde masero kubatsira kugadzira pezvakaitwa kufema uye kumedza. Mukuwedzera, vanoita kuti kuchaitwa ptosis iri pfupi zvichibvira nguva.

Yawapiwa uye kakawanda kwokubatsira hunde masero mumuviri zvinogona chete basa ruzivo nyanzvi!

Kushurudzira remangwana

Kunyange muzana remakore rapfuura, zvokuongorora kuti "Myasthenia" zvaireva kufa nokukurumidza. Asi nguva inopfuura, uye mushonga haamiri achiri. Panguva iyoyo, isu yakatanga zvakasiyana siyana anokosha anobatsira kuponesa upenyu uye maximize nguva kanganwiro.

Panguva iyoyo hatifaniri kukanganwa kuti myasthenia gravis ane chirwere. Izvi zvinoreva kuti varwere achava dzose nguva kune kurapwa (kana kugara prices) kuramba utano. Hazvina kuoma kuti zvokufungidzira kuti kunaka muupenyu iyi inogona yekudyidzana kutambura.

Naizvozvo zvakafanira kudzokorora kuti chete nenguva chirwere chirwere chingamise kunoita yayo nenguva tsika uye kudzivisa matambudziko.

kuitazve dziviriro

Takataura pamusoro zvokurwara ichi sezvo myasthenia gravis. Chii, chii achiperekedzwa zviratidzo chirwere uye kana pane zvinobudirira pakurapa chirwere, inokurukurwawo. Pakupedzisira ndinoda kugara pamusoro nzira kuitazve dziviriro, sezvo varwere, nhamba iri akakodzera chaizvo.

Chokutanga, kukosha mashoko pamusoro nhoroondo kusvika wetsinga. Muchiitiko chino, chero zvazvingava anogona kurasikirwa vakaronga nzira, asi chiitiko zviratidzo vanofanira kutaura chiremba vachirwa, kwete kumirira chinotevera kushanya.

Chechipiri, zvinokosha kuongorora uye, kana zvakakodzera, chinja zvakajairika muupenyu hwako. Varwere myasthenia hapana mamiriro ezvinhu anofanira kuva kuneta, saka zviri here kusarudza basa, kuvapa basa mupfungwa. Kana zvichibvira, unofanira kutirambidza nguva rwacho, kunyanya panyaya mabhazi.

Hatifaniri kukanganwa kuti chero chirwere, kunyange SARS, anoita muviri mupfungwa uye nokuvhiringidzirwa dziviriro yezvirwere mumuviri. Saka zvinokosha kuti kunyatsotevera kuongorora mamiriro utano hwavo, kudzivirira hypothermia uye kwete kuti munzvimbo yakakura kuwanda vanhu munguva mukuru kupararira kwezvirwere zvinotapukira.

In pamberi myasthenia gravis kugamuchira chero mushonga anofanira kubvumirana chiremba wako, nekuti pane chinokosha contraindications zhinji (vamwe akarangarira kubva pamusoro pavo).

Regai kuzvidzora medicate uye uve noutano hwakanaka!

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