UtanoMedicine

Hepatolienal syndrome: zviratidzo, kurapwa

"Syndrome" muchiGiriki zvinoreva "kubatana" kana kuti "kubatana." Muchirapa, chimiro ichi chinopiwa kune zvirwere zvine imwe nhamba yezvinhu zvinozivikanwa, kazhinji kuonekwa pamwe chete. Nokudaro, huwandu hwezviratidzo zvisati zvave kunyatsoongororwa hunogona kunyatsonzi chirwere. Chimwe chezvinhu izvi hepatolienal syndrome.

Nyaya

Hepatic-splenic syndrome ndiro zita rechipiri chechiitiko ichi. Iyo inoratidzika nekuwedzera mune chiropa uye spleen, zvakatarisana, basa rezvikamu izvi rinokanganiswa. Hepatolyenal syndrome inowanikwa mune zvirwere zvisingaperi zvehepatobiliary system uye zvinetso zvekupararira kweropa mu "portal vein-splenic vein" system.

Kupararira kwehuputi muropa uye spleen kunopa tsanangudzo yekuti nhengo idzi dzakabatanidzana sei uye kuti dzinosangana sei nekudengenyeka kwakadaro sa hepatolyenal syndrome. Zvinokwanisika kutsvaga kuwirirana kwevenous kwezvi nhengo idzi.

Mhemberero huru ndiyo portal. Iyo inounganidza ropa kubva padheka uye dzimwe nhengo dzomuviri wemimba. Ipapo inopinda muchiropa, iyo inogadziriswa inokonzera tsvina uye inotakura mishonga kuburikidza nemuviri. Chikamu chemukova wepachikova ndeye splenic, saka spleen iri muhukama hwepedyo nechiropa uye zvinenge zvichiitika mazviri. Izvi zvinotsanangura kuti nei hepatolienne syndrome inokanganisa chiropa uye spleen.

Pathogenesis yehepatolienal syndrome

Kuvhiringidzwa kweropa kunopinda kunogona kuitika nekuda kwekudzikisa chiedza chemukova wekutsvaga. Ikoko kune kupera kweropa uye, semugumisiro, kuwedzera kweropa. Sei izvi zvichiitika? Heano zvimwe zvikonzero:

  1. Kunyoreswa kwekunze kweropa remasuo. Izvi zvinogona kuitika mukati mechiropa uye pa hepatoduodenal ligament pamusuo wegori. Muchiitiko ichi, zviratidzo zve hepatolienal syndrome zvinogona kuonekwa nehosha dzakadaro:
  • Kurwisa kwechiropa.
  • Nzira yakasimba yehepatitis.
  • Thrombosis yemasipirini emasikirini uye pedyo nemakwenzi makuru.
  • Chirwere chepamusoro chechiropa chechiropa.
  • Chirwere chepfungwa cheruoko rworudyi rwemoyo.
  • Zvirwere zveBate ducts, matumire uye makrisiti.
  • Thrombosis ye hepatic veins.

2. Kupenya kwechiedza chemuviri:

  • Thrombosis yemasuo epasuo uye matavi awo makuru.
  • Thrombosis ye hepatic veins, kana kuti Badda-Chiari Syndrome.

Mukuwedzera kune zvinhu zvinokuvadza izvo zvinogona kukonzera kuwedzera muropa uye spleen, zvinogona kuitika sekudzivirira kudzivirira kusvika kwekupinda kwemakemikari.

Zvikamu zve

Kune zvikamu zvakasiyana zve hepatolyenal syndrome:

  1. Chikamu chekutanga chinogona kutora makore akawanda. Mamiriro ezvinhu ose anogutsa, anemia anononoka, anokoneni uye neutropenia anoonekwa. Chiropa hachina kukwidziridzwa, asi chinova chikuru kudarika spleen.
  2. Chikamu chechipiri chinoratidzwa nekuwedzera kwechiropa. Pane zviratidzo zvekuputsa kwehutano hwavo. Inogona kugara kwemwedzi inoverengeka.
  3. Chikamu chechitatu. Nguva yaro inenge gore rimwechete. Chimiro chekuita, kuderedza uye kuwirirana kwechiropa, kuperevedza kweanemia kunowedzera, pane zviratidzo zvehutachiona, ascites, kubuda kwemimba, varicose veine yepopu.
  4. Chikamu chechina. Chimiro chekuora mwoyo zvakakwana, kuzvimba uye zviratidzo zvekubuda ropa.

Zvinokonzera

Kazhinji kacho, hepatolyenal syndrome inowanikwa muvana.

Zvinokonzera vana nevakuru zvinogona kunge zvakasiyana:

  • Hereditary diseases.
  • Zvirwere zvinotapukira.
  • Congenital hemolytic anemia.
  • Congenital uye akawana zvirwere zvemukova wekutsvaga, spleen.
  • Hemolytic chirwere muchechecheche.
  • Kunyanya kunwa doro.

Mapoka evanhu vane ngozi uye zviratidzo zvavo

Zvirwere zvose zvinogona kukonzera hepatolyenal syndrome zvinogona kugoverwa mumapoka:

  1. Yakanaka uye isingaperi yechiropa chirwere. Iri boka rine marwadzo kana manzwiro ekuremara mune zvakanaka hypochondrium, dyspeptic disorders, itching, jaundice. Zvikonzero zvinogona kuendeswa kuhutachiona hwehupatachi, kusangana nevarwere vanopfurikidza, tsvina kana kuvhiyiwa, kudhakwa kwenguva refu, kushandiswa kwemishonga yehepatoxic, kurwadziwa kwakanyanya mudumbu, fivha.
  2. Denda rekuunganidza. Vanowanikwa pakati pemhuri yemhuri imwechete kana hama dzepedyo.
  3. Zvirwere zvinotapukira uye zvechirwere. Inopindirana nekunzi kudhakwa, fever, arthralgia uye myalgia.
  4. Zvirwere zvemwoyo yematambudziko. Izvo zvinotungamirirwa ne tachycardia, chirwere chemwoyo chinonzi ischemic, kuunganidzwa kwemvura mumvura yepiciciddial, kuwedzera uye kuchinja mukugadzirisa kwemoyo.
  5. Zvirwere zveropa uye maronda e-lymphoid. Nokuti boka iri rinoratidzwa nezviratidzo zvakadai sekushaya simba, fivha, kuwedzera kwemakirini.

Symptomatics

Kana murwere ane hepatolienal syndrome, zviratidzo zvinogona kunge zvinotevera:

  1. Kuwedzera kwechiropa uye spleen. Zvinorwadza zvinorwadza mu palpation.
  2. Weight reduction.
  3. Basa rezvinyorwa zve endocrine zvinokanganiswa.
  4. Matambudziko mumugwagwa wezvokudya.
  5. Anemia. Pale uye yakaoma ganda.
  6. Zvinokwanisika kuwedzerwa kwemvura mumakumbo emimba.
  7. Uturu uye hutano huri pamwe.
  8. Yellowing yeprotein coat yemaziso.
  9. Tachycardia, kupera kwekufema.
  10. Fragility yezvipikiri, kusuruvara kwemvere.

Kuita kuti kuongororwa kunofanirwa kuongorora, uye nekuongororongedzwa kwakanyanya kwezvikamu - kuongororwa.

Diagnostics

Apo zviratidzo zviri pamusoro apa zvinoitika, kusiyana kwekusiyanisa kwehepatomegaly uye hepatolenal syndrome kunoitwa. Kuti uite izvi, unofanirwa kushandisa zvakasiyana-siyana zvemabasa. Chimwe chezvinhu zvokutanga ndechekuongorora ropa kwepamusoro uye chidzidzo chehupenyu hwehupenyu. Kuti aratidze chikonzero che hepatolyenal syndrome, kusiyana kwekutsvaga kunongoda chete. Muchikamu chayo maitiro anotevera anoitwa:

  • Kushandura kwechiropa uye chirwere chenduru, chirwere chenduru, midziyo yemudumbu.
  • Computer tomography.
  • Kuongorora kwechiropa uye spleen.
  • X-ray kuongorora kwe duodenum.
  • Laparoscopy.
  • Nguva yakagadziriswa yechiropa uye spleen.
  • Kudzidza kwemapfupa emarara uye lymph nodes.

Parizvino, sayenzi haina kumira uye urongwa hwekuongorora huri kuramba huchiwedzera mukuongororwa kwechiitiko chakadai se hepatolienal syndrome. Differential diagnosis Chirwere chikuru, kufunga nezvechirwere chemukati uye chiropa chemuviri Nekuvapo kwayo ndiyo basa guru.

Kurapa uye zvinetso zvechirwere

Semitemo, chirwere chehepatolienal syndrome ndechokuona chinokonzera chirwere chepfungwa uye kurapa kwayo. Haisi chirwere chokuzvimirira. Kana iwe ukaonekwa kuti une "hepatolyenal syndrome," kurapa kunofanira kutungamirirwa ne gastroenterologist. Muchiitiko ichi, hepatoprotectors, antiviraire, mahomoni uye mavitamini anoshandiswa. Munyaya imwe neimwe, panofanira kuva nemunhu oga, achitarisa etiology yechirwere.

Kana iwe uchingorasikirwa nechirwere uye usingaiti, chirevo chacho chinogona kushungurudza. Zvinetso zvechirwere ichi ndezvechirwere chechiropa, chirwere chechiropa chechiropa, kuputika kweguruvladder, zvirwere zveropa. Mumamiriro ezvinhu akadaro, kubviswa kwezvikamu zvechiropa uye spleen kana nhengo transplantation uye kuwedzerwa ropa kunogoneka.

Pachigamba chekutanga, varwere vanogona kushanda uye vanogona kukunda zvishoma zvishoma. Mune ramangwana, kana mamiriro acho achiwedzera, murwere anove akaremara.

Kudzivirira

Kuti urege kukanganisa kutanga kwekurapa, zvinodiwa:

  • Nguva dzose tora ropa uye urini miedzo.
  • Nokufamba kwenguva, unoongorora, kunyanya kana iwe uri pangozi.
  • Kudzivirira hepatolienal syndrome kunosanganisira kurwisa zvikonzero zvinokonzera chiropa uye zvirwere zvepleen.
  • Zvinotarisirwa kuenderana nehurumende yezvokudya zvakakodzera, kuitira kuti zvokudya zvive nemuwandu hunodiwa wemafuta, mapuroteni uye makhahydrates uye, zvechokwadi, mavitamini.
  • Usashandisa doro zvisina kufanira, kusvuta uye kutungamirira mararamiro akanaka.

Izvo hazvina zvirwere zvisingaiti, uye kunyanya kana zvichitaura nhengo dzakakosha sechiropa uye chirwere. Kuziva kwenguva pfupi dambudziko, uye ipapo kurapa kwakakwana kunogona kubudirira.

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